SİNAN DEMİRCİOĞLU, Ali DOĞAN, Murat ALTINBAŞAK, CENGİZ DEMİR

Primer Plazma Hücreli Lösemi: Olgu Sunumu

Plazma hücreli lösemi (PHL), plazma hücreli diskrazilerin nadir görülen bir formudur. Primer ve sekonder PHL olmak üzere iki formu vardır. Prognozu oldukça kötüdür. Morfolojik olarak matür plazma hücrelerine benzememesi sebebiyle tanıda karışıklıklar olabilmektedir. Tedavide bortezomib bazlı rejimler ve otolog kök hücre nakli önerilmektedir.

Primary Plasma Cell Leukemia: Case Report

Plasma cell leukemia (PHL) is a rare form of plasma cell dyscrasias. There are two forms of primary and secondary PHL. The prognosis is very poor. Since the morphology does not resemble mature plasma cells, there may be confusion in the diagnosis. Bortezomib based regimens and autologous stem cell transplantation are recommended for treatment.

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