PFAPA SENDROMU - ORAL BULGULARI VE DENTAL TEDAVI PROTOKOLÜ

Bu olgu sunumunda amaç, PFAPA sendromlu lenfadenopati şikayeti ile kliniğimize başvuran bir hastanın, klinik ve radyografik kayıtlarını rapor etmek ve ilgili literatürleri gözden geçirmektir. PFAPA sendromu tekrarlayan ve periodik ateşlerle seyreden, ani başlayan yüksek ateş, aftöz stomatit, farenjit ve servikal lenfadenopati ile karakterize bir sendromdur. Genellikle 5 yaş altı çocuklarda ani bir başlangıç gösterir. 10 yaş öncesi hastalığın kendiliğinden gerilediği bildirilmiştir. Oral bulgular arasında aftöz stomatit bulunması sebebiyle hastalar çocuk diş hekimine sıklıkla başvurur. Olgumuzda PFAPA sendromu tanısı konulmuş kronolojik yaşı 6 yaş 7 ay olan kız hastanın oral bulguları, büyüme ve gelişimi değerlendirilmiştir. Hastalığın ağız içi bulguları ve ataklar esnasında geçirilen febril konvülsiyonlar nedeniyle, bu hastalarda özel bir diş hekimliği yaklaşımı gerektirir. Anahtar Kelimeler: PFAPA Sendromu, aftöz stomatit, lenfadenopati PFAPA SYNDROME - ORAL MANIFESTATIONS AND A DENTAL TREATMENT PROTOCOLABSTRACTThe purpose of this case report is to report the clinical and radiographic records of a patient who applied to our clinic with PFAPA syndrome and with cervical lymphadenopathy complaints, and also to review the relevant literature.Periodic Fever, Aphthous Stomatitis, Pharyngitis, Cervical Adenitis (PFAPA) is a recurrent syndrome that consists of episodic fever and characterized by abruptly starting fevers, aphthous stomatitis, pharyngitis, and cervical lymphadenopathy. PFAPA usually starts suddenly in the children under the age of 5 years. However, it has been reported that the disease had been resolved by itself, after the age of 10 years. Since aphthous stomatitis is among the oral symptoms, patients frequently apply to pediatric dentistry clinics.In our case report, growth and development and oral findings of a girl diagnosed with PFAPA and with a chronological age of 6 years 7 months, were evaluated. Due to the oral manifestations of PFAPA and febrile convulsion attacks, a special dental approach is required to the patients with PFAPA. Key Words: PFAPA syndrome, aphthous stomatitis, lymphadenopathy

Anahtar Kelimeler:

PFAPA Sendromu, aftöz stomatit

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