Magnetic resonance imaging findings of Susac syndrome
Susac sendromu patogenezi bilinmeyen nadir bir hastalıktır. Beyin, retina ve kohleanın etkilendiğimikroanjiyopati sonucunda ortaya çıkar. Bu durum hastalığın tipik triadı olan subakutensefalopati, retinal arteriollerin tıkanmasına bağlı oluşan görme kaybı ve sensorinöral işitmekaybına neden olur. Manyetik rezonans görüntüleme, retinal floresan anjiografi ve odyografibulguları tanıya yardımcıdır. Erken tedavi sekel oluşumunu azaltabilir ve iyileşemeyihızlandırabilir. Bu yazıda hastalığın tüm bulguları ile birlikte bir Susac sendromlu olguyusunuyoruz.
Susac sendromunun manyetik rezonans görüntüleme bulguları
Susac syndrome is a rare disease of unknown pathogenesis. It is caused by a microangiopathyaffecting the arterioles of the brain, retina, and cochlea, giving the classic clinical triad of subacuteencephalopathy, visual loss secondary to retinal branch occlusions, and sensorineural hearing loss.Magnetic resonanace imaging, retinal fluorescein angiography, and audiography findings enablediagnosis. Early therapy may reduce sequelae and improve recovery. Herein we report a case ofSusac syndrome with all the findings of the disease.
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