Serdal KORKMAZ, Mehmet ŞENCAN, Ayşe ÇİÇEKLİ AKBULUT, Ruhiye CEVİT, Hatice TERZİ

Oksipital kemik yerleşimli langerhans hücreli histiyositozis: Olgu sunumu

Langerhans Hücreli Histiyositozis aynı histopatolojiye sahip fakat farklı klinik semptomlara nedenolan hastalıklar grubu olarak adlandırılmaktadır. Üç ayrı formu olan hastalığın lokalize formuEozinofilik granulom olarak isimlendirilmektedir. Eosinofilik granülom, Langerhans HücreliHistiyositozis grubu içerisinde klinik seyri en az şiddetli ve lokalize form olup en iyi prognozasahip alt tiptir. Tedavi şeçenekleri arasında, cerrahi eksizyon, kemoterapi, radyoterapi tek başınakullanılabileceği gibi kombine kullanımları da bulunmaktadır. Burada, sağ oksipital bölgede şişlikve ağrı şikayeti ile kliniğimize başvuran, radyolojik tetkikleri ve histopatolojik incelemesisonucunda Langerhans Hücreli Histiyositozis (Eosinifilik granülom) tanısı alan genç erişkin birhasta sunuldu.

Involvement of occipital bone in langerhans cell histiocytosis: A case report

Langerhans Cell Histiocytosis is termed as a group of diseases that leads to have samehistopathology, but different clinical symptoms. The disease has 3 distinct forms and the localizedform is termed as Eosinophilic granuloma . Eosinophilic granuloma is the localized form of whichhas the least clinical severity and the most favourable subtype in Langerhans Cell Histiocytosisgroup. The treatment options are available as surgery removal, chemotherapy, and radiotherapyalone or in combinations. In this paper, a young adult patient was represented who referred to ourclinic with complaints of swelling and pain on right occipital region, and who diagnosed asLangerhans Cell Histiocytosis (Eosinophilic granuloma) after evaluation of radiologic tests andhistopathologic survey.

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