Eylem Yaman PINARCI, Aysel PELİT, Duygu BOZKIRLI, Emine Tuba CANBOLAT

Primer Sjögren sendromu: Olgu sunumu

Bu vaka ile kuru gözde sistemik değerlendirmenin ve hastalığın ciddiyetine göre tedavi seçiminin önemi vurgulandı. Kırksekiz yaşında kadın hastanın yaklaşık yirmi yıldır var olan ve giderek kötüleşen yanma, kaşıntı ve görme azlığı şikayetleri vardı. Schirmer I test sonuçları iki gözde 0mm/5 dakika idi. Ön segment muayenesinde iki gözde filamentöz keratit saptandı. Sjögren sendromu tanısı için yapılan lakrimal bez biyopsisi ve serumda Anti-Ro/ SSA, anti-La/ SS-B antikorları pozitifti. Hastanın tedavisine geçici punktum tıkaçları ve oral hidroksiklorokin eklendi..10 gün sonra göz kuruluğu şikayetleri geriledi ve iki göz alt punktumuna kalıcı plaklar yerleştirildi. Tüm kuru göz hastaları sistemik olarak değerlendirmeli ve tedaviden önce hastalığın ciddiyeti belirlenmelidir. Sjögren sendromuna bağlı kuru göz tedavisinde yerine koyma tedavisine ek olarak punktum tıkacı uygulaması da uygun bir seçenektir.

Anahtar Kelimeler:

kuru göz sendromu, punktum tıkama, Sjögren sendromu

Primary Sjögren Syndrome: Case report

The importance of systemic evaluation of dry eye patients and choosing appropriate treatment based on the severity of disease were emphasized with this case. 48 years old woman complained about decreased vision, burning, itching in both eyes which got worse over the years, for about 20 years. Schirmer I test value was 0 mm/5min in both eyes. Slit lamp examination revealed filamentary keratitis in both eyes. Anti-Ro/ SSA, anti-La/ SS-B antibodies and salivary gland biopsy for Sjögren syndrome were positive. Temporary punctal occlusion and oral hydroxychloroquine were added to her treatment. After 10 days, her overall dry eye condition improved and permanent punctual plugs were inserted in both lower puctums.Dry eye patients should be evaluated systemically and severity of disease should be considered before treatment is started. Addition to topical application of artificial tears, punctal occlusion may be a proper option in dry eye patients with Sjogren syndrome.

Keywords:

dry eye syndrome, punctual occlusion, Sjogren syndrome,

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Yazışma Adresi / Address for Correspondence: Dr. Aysel Pelit Başkent Üniversitesi Tıp Fakültesi Göz Hastalıkları Anabilim Dalı e-mail: aypelit@yahoo.com geliş tarihi/received :12.05.2013 kabul tarihi/accepted:31.05.2013