İlknur SÜRÜCÜ KARA, Mustafa ÖZDAMAR, Abdulkerim KOLKIRAN, Necla AYDIN PEKER, İsmail TOPAL

Intussusepsiyon Henoch-Schonlein purpurası'nın ilk tezahürü olabilir mi?

Henoch-Schönlein purpurası, çocukluk çağının en sık görülen lökositoklastik vaskülitidir. Derinin küçük damarlarında, eklemlerde, gastrointestinal sistemde ve böbreklerde immünoglobulin A birikir. Ciltte palpe edilebilen purpura genellikle ilk bulgudur ve genellikle alt ekstremiteler ve kalçada görülür. Eklemler etkilenebilir, böbrekler etkilenebilir. Gastrointestinal sistem şikayetleri genellikle purpurik döküntüden bir hafta sonra ortaya çıkar. Sindirim sisteminin en sık görülen klinik özellikleri karın ağrısı ve kusmadır. Sindirim sisteminin tutulumunda intussusepsiyon insidansı yaklaşık % 1-5' tir. Ancak, intussusepsiyon ilk belirti değildir. Bizim olgumuzda karın ağrısı ve intussusepsiyon ilk bulgulardır. Operasyondan üç gün sonra tipik döküntüler gözlenmiştir.

Anahtar Kelimeler:

Henoch-Schonlein purpurası, intussusepsiyon, çocuklar, vaskülit

Could intussusception be the first manifestation of Henoch-Schonlein purpura?

Henoch-Schönlein purpura, leukocytoclastic vasculitis is the most common vasculitis of childhood. Immunoglobulin-A accumulates in the small veins of the skin, joints, gastrointestinal tract and kidney. The involvement of the skin in palpable purpuric rash is usually the first finding and basically shows the lower extremities and hips. Joints can be affected, kidneys can be affected. Complaints of gastrointestinal system usually occur one week after purpuric rash. The most common clinical features of the digestive system are abdominal pain and vomiting. The incidence of Intussusception in digestive tract involvement is about 1-5%. However, intussusception is not the first symptom. In our case, abdominal pain and Intussusception are the first findings. Typical rash appeared three days after operative. Second case in literature.

Keywords:

Henoch-Schonlein purpura, Intussusception, children, vasculitis,

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