Çocukluk çağında idiyopatik spontan bilateral adrenal kanama

Adrenal kanama çoğunlukla yenidoğan döneminde görülse de daha büyük çocuklarda ve erişkinlerde de olabilmektedir. Etiyolojide birçok neden rol oynamakta ve klinik bulgu ve belirtiler çeşitlilik gösterebilmektedir. Sunulan vakada masif adrenal kanamaya rağmen adrena yetersizlik gözlenmemiş ve herhangi bir etiyolojik faktör bulunamamıştır. Bilgilerimize göre literatürdeki çocukluk çağında spontan idyopatik bilateral masif adrenal kanaması olan ancak adrenal yetersizlik gelişmeyen ilk vaka olma özelliğini taşımaktadır.

Spontaneous idiopathic bilateral adrenal hemorrhage in a pediatric patient

Adrenal hemorrhage occurs most frequently in the newborn, but it has been also well documented in older children and adults. There are several reasons in etiology and clinical symptoms can vary widely depending on the residual adrenal function. In this case; despite bilateral massive adrenal hemorrhage, no etiologic factor had been found and adrenal insufficiency was not present. To our knowledge, our patient is a spontaneous idiopathic bilateral massive adrenal hemorrhage case without adrenal insufficiency which is the first one reported in a pediatric patient in literature.

Keywords:

Spontan idyopatik bilateral adrenal kanama; çocukluk çağı; adrenal yetmezlik,

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