Şebnem KADER, Mehmet SARIAYDIN, Mehmet MUTLU, Yakup ASLAN, Mustafa İMAMOĞLU, Ali AHMETOĞLU

Neonatal Kolestazın Ender Görülen Bir Nedeni: Tip IVA Koledok Kisti

Koledok kistleri ekstrahepatik ve/veya intrahepatik safra yollarının kistik dilatasyonu ile karakterize ender kolestaz nedenlerindendir. Neonatal kolestaz tanısı alan hastalarda ultrasonografi ile anatomik yapıların değerlendirilmesi, koledok kisti gibi ender görülen anormalliklerin saptanma- sını sağlayarak erken dönemde hastalığın tedavi edilmesini ve ciddi komplikasyonların gelişmesini önleyebilir. Bu vaka raporunda, neonatal kolestazın ender bir nedeni olarak Todani sınıflamasına göre Tip IVA koledok kisti olgusu sunulmuştur

Anahtar Kelimeler:

Yenidoğan, kolestaz, Todani sınıflaması, Tip IVA koledok kisti

A Rare Cause of Neonatal Cholestasis: Type IVA Choledochal Cyst

Choledochal cyst is a rare cause of cholestasis characteri- zed by cystic dilatation of extrahepatic and/or intrahepatic bile ducts. Sonographic evaluation of anatomical structu- res in patients with neonatal cholestasis, can detect bile duct abnormalities such as rarely seen choledochal cysts and enable treatment of the disease in the early stages which may prevent the development of serious complicati- ons. In this case report, a patient with Type IVA choledoc- hal cyst according to Todani classification which is a rare cause of neonatal cholestasis is presented

Keywords:

Newborn, cholestasis, Todani classification, Type IVA choledochal cyst,

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dick MC, Mowat AP. Hepatitis syndrome in infancy--an epidemiological survey with 10 year follow up. Arch Dis Child 1985;60:512-6. http://dx.doi.org/10.1136/adc.60.6.512
Moyer V, Freese dK, Whitington PF, olson Ad, Brewer F, Colletti rB, et al. Guideline for the evaluation of cholestatic jaundice in infants: recommendations of the North American Society for Pediatric Gastroenterology, Hepatology and Nutrition. J Pediatr Gastroenterol Nutr 2004;39:115-28. http://dx.doi.org/10.1097/00005176-200408000-00001
Zhen C, Xia Z, long l, lishuang M, Pu y, Wenjuan Z, et al. Laparoscopic excision versus open excision for the treat- ment of choledochal cysts: a systematic review and meta- analysis. Int Surg 2015;100:115-22. http://dx.doi.org/10.9738/INTSURG-D-14-00165.1
Choledochal cysts: analysis of disease pattern and optimal treatment in adult and paediatric patients. HPB (Oxford) ;9:383-7. http://dx.doi.org/10.1080/13651820701646198 concept of etiology. Am J Roentgenol Radium Ther Nucl Med ;119:57-62. http://dx.doi.org/10.2214/ajr.119.1.57 features and classification. Am J Gastroenterol 1985;80: 7.
Choledochal cyst: diagnosis in neonates. South Med J 1988;81: 8. http://dx.doi.org/10.1097/00007611-198812000-00024 de Vries JS, de Vries S, Aronson dC, Bosman dK, rauws
EA, Bosma A, et al. Choledochal cysts: age of presentation, symptoms, and late complications related to Todani’s classifi- cation. J Pediatr Surg 2002;37:1568-73. http://dx.doi.org/10.1053/jpsu.2002.36186
Jl. Choledochal cyst disease. A changing pattern of presenta- tion. Ann Surg 1994;220:644-52. http://dx.doi.org/10.1097/00000658-199411000-00007
Singham J, yoshida EM, Scudamore Ch. Choledochal cysts: part 2 of 3: Diagnosis. Can J Surg 2009;52:506-11.
Samuel M, Spitz l. Choledochal cyst: varied clinical presen- tations and long-term results of surgery. Eur J Pediatr Surg ;6:78-81. http://dx.doi.org/10.1055/s-2008-1066476 tract cancer. Ann Surg Oncol 2007;14:1200-11. http://dx.doi.org/10.1245/s10434-006-9294-3 al. Early and late results of excision of choledochal cysts. J Pediatr Surg 1997;32:1563-6. http://dx.doi.org/10.1016/S0022-3468(97)90453-X