Sibel ERTAN, Hülya APAYDIN, Naci KOÇER, Sibel ÖZEKMEKÇİ

Olası bir idyopatik intrakraniyal pakimenenjit olgusunun iki yıl süreli izlemi

Bu yazıda, tekrarlayıcı multipl kranyal sinir felçleri gelişmiş olan, radyolojik tetkikleri pakimenenjitle uyumlu bulunan ve inisiyal semptomatik steroid yanıtının daha sonraki ataklarda alınamadığı bir kadın hastanın 2 yıl süreli klinik ve radyolojik izlemi sunulmuştur. Herhangi bir etyolojik sebebin belirlenememesi nedeniyle olası idiyopatik hipertrofik pakimenenjit (İHP) tanısı alan hasta özelinde, gerek klinik, gerekse radyolojik açıdan İHP'nin ayırıcı tanısında ele alınması gereken diğer hastalıklar, oldukça nadir rastlanılan İHP'ye ait mevcut literatür bilgisi ışığında tartışılmıştır.

A case with probable idiopathic intracranial pachymeningitis: Two years follow up

Background.- Idiopathic hypertrophic cranial pachymeningitis is a rare inflammatory disease of the dura mater of unknown origin with frequent recurrences, progressive cranial nerve palsies and headache despite initial response to steroid therapy and may cause sequels. Observation.- We report a two-year follow-up of a patient having recurrent multiple cranial nerve palsies whose radiological and clinical features were consisted with pachymeningitis Her initial symptomatic response to steroids disappeared during the course of the disease. In accordance with the patient who had the diagnosis of idiopathic hypertrophic pachymeningitis (IHP) due to absence of any etiological causes, we discussed the diseases to be considered in the differential diagnosis of IHP.

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