ÇOCUK YOĞUN BAKIM ÜNİTESİNE YATAN DOWN SENDROMLU HASTALARIN KLİNİK ÖZELLİKLERİ: 6 YILLIK DENEYİMLERİMİZ The Clinical Features of Down Syndrome who is Admitted to the Pediatric Intensive Care Unit: 6 Year Experiences

Amaç: 2010-2016 yılları arasında Erciyes Üniversitesi Çocuk Yoğun bakım Servisi’ne yatmış olan Downsendromlu hastaların yatış endikasyonları ile mortalite ve morbiditeye eşlik eden faktörlerin değerlendiril-mesi amaçlandı.Gereç ve Yöntem: Çalışmaya Ocak 2010–Aralık 2016 tarihleri arasında Çocuk Yoğun bakım ünitesine ya-tırılan 25 Down Sendromu tanılı hasta alındı. Tüm hastaların başvuru yaşı, cinsiyet, ek anomalileri, ameliyatvarlığı ve klinik seyirleri kaydedildi. Hastaların sistemik fizik muayeneleri yapılıp Down sendromuna ilişkinbulgular açısından başta kardiyovasküler sistem olmak üzere tüm sistemler ayrıntılı olarak değerlendirildi.Bulgular: Tüm kardiyak defektler görülme oranlarına göre ventriküler septal defekt (VSD) %32, patentduktus arteriosus (PDA) %4, atriyal septal defekt (ASD) %12, atriyoventriküler septal defekt (AVSD) %16,fallot tetrolojisi (TOF) %4, mitral yetmezlik %4, triküspit atrezisi %4, mitral yetmezlik + triküspit yetmezliği%8 şeklinde idi. Çalışmamıza dahil ettiğimiz hastaların 15’inde (%60) pulmoner hipertansiyon tespit edildi.Pulmoner hipertansiyon ile mortalite arasında anlamlı bir ilişki saptandı. (p

The Clinical Features of Down Syndrome who is Admitted to the Pediatric Intensive Care Unit: 6 Year Experiences

Background: The aim of this study was to evaluate the indications for hospitalization and the factors associated with mortality and morbidity in patients with Down syndrome who were hospitalized in the Erciyes University Pediatric Intensive Care Unit between 2010-2016. Material and Methods: 25 Patients with Down Syndrome who were admitted to the Pediatric Intensive Care Unit between January 2010 and December 2016 were included in the study. The age, sex, additional anomalies, operation status and clinical course of all patients were recorded. Systematic physical examinations of the patients were performed and all systems, especially the cardiovascular system, were evaluated in detail in terms of findings related to Down syndrome. Results: The ratio of cardiac defects type which we detected in our patients are ventricular septal defect (VSD) 32%, patent ductus arteriosus (PDA) 4% and atrial septal defect (ASD) 12%, atrioventricular septal defect (AVSD) 16%, tetroloji of Fallot (TOF) 4%, mitral regurgitation 4%, tricuspid atresia 4%, mitral regurgitation + tricuspid regurgitation 8%. Pulmonary hypertension was detected in 15 (60%) of the patients included in our study. There was a significant relationship between pulmonary hypertension and mortality. (p

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