Charcot-Marie-Tooth Hastalığında Bilateral Pençe-Elin Düzeltilmesi İçin Ortez : Olgu Sunumu

Charcot-Marie-Tooth (CMT) yaygın görülen kalıtsal periferik sinir bozukluğudur. CMT’li hastalarda daha çok alt ekstremite deformiteleri görülmesine rağmen sıklıkla pençe-el deformitesi ve maymun eli deformiteleri de görülmektedir. Bu deformiteler düzeltilmediği takdirde elin biyomekaniğini bozmaktadır. Bu deformitelerin düzeltilmesinde sıklıkla termoplastik materyalden yapılan ortezlerden yararlanılmaktadır. Bu vakamızda CMT’li bir hastada meydana gelen bilateral claw-el deformitesine uygulanan lumbrikal bar ortezinin sonuçları sunulmuştur. Ortez kullanımı öncesi ve sonrası el becerisi Purdue Pegboard testi ile, el kavrama kuvveti manuel el dinamometresi ile pinç kuvveti ise pinçmetre ile değerlendirilmiştir. Yapılan değerlendirmeler sonucunda lumbrikal bar ortezinin pençe-el deformitesini düzelttiği ancak el kavrama kuvveti, pinç kuvveti ve el becerileri üzerinde iyileşmelere sebep olmadığı görülmüştür.

Anahtar Kelimeler:

Charcot-Marie-Tooth, Lumbrikal bar ortezi, Pençe-el

Orthosis For Correction Of Bilateral Claw-Hand In Charcot-Marie-Tooth Disease: A Case Report

Charcot-Marie-Tooth (CMT) is a common inherited peripheral nerve disorder. Although lower extremity deformities are more common in patients with CMT, claw-hand deformities and monkey hand deformities are also frequently seen. If these deformities are not corrected, they impair the biomechanics of the hand. Orthoses made of thermoplastic material are often used to correct these deformities. In this case, the results of the lumbrical bar orthosis applied to the bilateral claw-hand deformity in a patient with CMT are presented. Before and after orthosis use, dexterity was evaluated with the Purdue Pegboard test, hand grip strength was evaluated with a manual hand dynamometer, and pinch strength was evaluated with a pinchmeter. As a result of the evaluations, it was seen that the lumbrical bar orthosis corrected the claw-hand deformity, but did not cause improvements in hand grip strength, pinch strength and dexterity.

Keywords:

Charcot-Marie-Tooth, Lumbrikal bar ortezi, Pençe-el,

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