Reşit Doğan KÖSEOĞLU, Arzu ENSARİ, Yaşar AYVA

Early colon carcinoma of the appendix associated with adenomatous polyposis coli: a case report

Adenomatöz polipozis koli kolonda yüzlerce adenomatöz polip varlığı ile karakterli otozomal dominant bir hastalıktır. Bununla beraber bu sendromda poliplerin apendiks vermiformis lokalizasyonu ve appendiks lokalizasyonlu poliplerde malign transformasyon çok nadirdir. Burada, appendiks vermiformis lokalizasyonlu polip ve kolondaki bazı poliplerde intramukozal kanser odakları gösteren bir adenomatöz polipozis koli olgusunu sunuyoruz.

Adenomatöz polipozis koli ile ilişkili apendiksin erken kolon karsinomu: olgu sunumu

Adenomatous polyposis coli (APC) is an autosomal dominant disorder characterized by the presence of hundreds of adenomatous polyps in colon. However, in this syndrome, appendiceal localization of the polyps and malignant transformation in appendiceal polyps are very rare. We report here, a case of adenomatous polyposis coli showed foci of intra mucosal cancer in the appendiceal polyp and some colonic polyps.

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