Fatih YALÇINKAYA, Fuat DEMİREL, Uğur ALTUĞ, Murat ÇAKAN

Bilateral nephron-sparing surgery for giant bilateral renal angiomyolipomas associated with tuberous sclerosis complex

Tuberosklerozis kompleksli hastaların önemli bir kısmında renal anjiomyolipom vardır. Bu hastalardaki lezyonlar bilateral olma ve daha hızlı büyüme eğilimindedir. Renal kanama ise bu hastalığın en çok korkulan komplikasyonudur. Biz multipl, bilateral dev renal anjiyomyolipomlara sahip tuberosklerozisli bir genç bayanda bilateral nefron-koruyucu cerrahi yaptık. Hastada önemli bir intraoperatif veya postoperatif komplikasyon gözlemedik. Bir yıllık takip süresince hastanın böbrek fonksiyonları normal olarak kaldı.

Dev bilateral renal anjiyomyolipom ve tuberosklerozis kompleksli hastada bilateral nefron-koruyucu cerrahi

A significant number of patients with tuberous sclerosis complex (TSC) have renal angiomyolipoma and these patients tend to have bilateral lesions grow more rapidly. Bleeding is the most fearful complication in the patients. We described a young woman with TSC and multiple bilateral giant renal angiomyolipomatosis. We performed bilateral nephron-sparing surgery (NSS) and did not see any significant intraoperative or postoperative complication. Renal function was normal in the first year of follow-up.

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