Masoud NASHİBİ, Parisa SEZARİ, Farhad SAFARİ, Ahmad NADERİ, Kamran MOTTAGHİ

Möebius Sendromu, Anestezi Uzmanının Nelere Dikkat Etmesi Gerekir: Olgu Sunumu

İlk kez 1888’de tarif edilen Möebius sendromu başlıca altıncı, 7. ve 8. kraniyal sinirlerin kombinasyonunu içeren kranial sinir felcidir. Nadir de olsa, etkilenen bebekler ve çocuklar birçok oftalmolojik veya otolojik cerrahi için anesteziyologlara yönlendirilebilir. Bu tür hastaların anestezik yönetimine ilişkin veriler azdır, olgu sunumları tüm dünyada anesteziyologlar için yararlı bir bilgi kaynağı olabilir. Yüz kaslarını ve gelişimini etkilediği için, etkilenen hasta potansiyel zor hava yolu olabilir, ancak nadirdir. Malign hipertermi başka bir potansiyel tehdittir. Genel anestezi altında kohlear implantasyon adayı bir Möebius sendromu olgusunu sunuyoruz. Olgumuz sorunsuz olmasına rağmen, bu hastalarda anesteziyoloji ekibi zor hava yolu yönetimi veya malign hipertermi gibi potansiyel risklere hazırlıklı olmalıdır.

Möebius Syndrome, What Anesthesiologist ID Should Consider About: A Case Report

First described in 1888, Möebius syndrome is a variety of cranial nerve palsy combinationsmainly involving sixth, seventh and eighth cranial nerves. Although rare, affected infants andchildren might be referred to anesthesiologists for many types of ophthalmologic or otologicsurgeries. Data on anesthetic management of such patients are scarce and case reports can be asource of useful information for anesthesiologists throughout the world.Since it involves facial muscles and their development, affected patient potentially may be a caseof difficult airway as well; although it is rare. Malignant hyperthermia is another potentialthreat.We report a known case of Möebius syndrome candidate for cochlear implantation under generalanesthesia.Although our case was uneventful, the anesthesiology team has to be prepared for potential riskssuch as difficult airway management or malignant hyperthermia in these patients.

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