Abdullah Barış AKCAN, Deniz İLGÜN, Sezen ÖZKISACIK, Ali Onur ERDEM, İbrahim METEOĞLU, Yasemin Durum POLAT, Münevver Kaynak TÜRKMEN

SOLUNUM SIKINTISI OLAN BİR YENİDOĞANDA AKLA GELMELİ – KONGENİTAL KİSTİK ADENOMATOİD MALFORMASYON?

Kongenital kistik adenomatoid malformasyon KKAM , primer bronşiyollerin düzensiz, hamartamatöz ve adenomatoid proliferasyonu ile karakterizedir.Kongenital akciğer malformasyonlarının %25’ini oluşturur ve yenidoğanlarda en sık solunum sıkıntısı ile ortaya çıkar. Bu yazıda prenatal tanısı olmayan ve yaşamın ilk saatlerinde solunum sıkıntısı semptomları gelişen bir vaka sunularak ender görülen KKAM ‘ın tartışılması amaçlandı

Should Come To Mind With a Newborn With Respiratory Distress - Congenital Cystic Adenomatoid Malformation?

Irregular, hamartomatous and adenomatous proliferation of the primary bronchioles characterizes Congenital Cystic Adenomatoid Malformation CCAM . It constitutes 25% of congenital pulmonary malformations and occurs mostly with respiratory distress syndrome in newborns. In this article, the rarely seen CCAM was aimed to be discussed by presenting a case without prenatal diagnosis and a case with symptoms of respiratory distress in the first hours of life

Keywords:

Congenital, cystic adenomatous malformation, newborn,

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