Fatıma Nur KOZHAN, Tezcan KAYA, Esma Seda ÇETİN, Alper KARACAN

Budd-Chiari Sendromu ile Prezente Olan Ampulla Vateri Tümörü

Budd-Chiari sendromu hepatik venöz çıkış yolunun tromboz veya flebit nedenli obstrüksiyonu ile oluşan nadir bir klinik tablodur. Etyolojisinde venöz dönüşü bozan hastalıklar, tromboza eğilim yapabilen durumlar veya vaskülit nedenleri yer almaktadır. Ampulla vateri adenokarsinomu gastrointestinal sistem malignitelerinin oldukça az görülen bir tümörüdür. Ampulla vateri tümörünün başlangıç aşamasında Budd-Chiari sendromuna neden olması ve birlikteliği nadir bir durumdur. Bu makalede asit, ikter nedeni ile yatırdığımız ve ampulla vateri tümörüne bağlı Budd-Chiari sendromu tanısı koyduğumuz bir olgu sunulmuştur.

Anahtar Kelimeler:

Ampulla Vateri, asit, Budd-Chiari Sendromu, tromboz

Tumor of the Ampulla of Vater Presented with Budd-Chiari Syndrome

Budd-Chiari syndrome is a rare clinical condition that characterized with hepatic venous outflow tract obstruction caused by thrombosis or phlebitis. Etiology includes diseases that disrupt venous return, conditions that can predispose to thrombosis, or causes of vasculitis. Adenocarcinoma of the ampulla of Vater is a rare tumor of gastrointestinal malignancies. It is very rare for tumor of the ampulla of Vater to cause and coexist with Budd-Chiari syndrome in its initial stage. In this article, we presented a case of Budd-Chiari syndrome associated with tumor of the ampulla of Vater which we were hospitalized due to ascites and icter.

Keywords:

Ampulla of Vater, ascites, Budd-Chiari syndrome, thrombosis,

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