Tuba GİRAY, Özlem CANTÜRK, Turgut AĞZIKURU, Gülay Çiler ERDAĞ, Neslihan ÇİÇEK, YASEMİN AKIN, Ayça VİTRİNEL

Jüvenil dermatomitozitli bir olgu sunumu

Jüvenil Dermatomiyozit (JDM); pediatrik miyopatilerin en yaygını olup, deri bulguları ve progresif olarak proksimal kaslarda zayıflığa yol açan, fokal miyozitlerle seyreden ve immünsupresif tedaviye cevap veren sistemik bir vaskülopatidir. En sık 5-14 yaşlar arasında görülür. 16 aylık bir olguyu yaşının küçük olması nedeniyle sunmak istedik.

Anahtar Kelimeler:

Dermatomiyozit, Kas hastalıkları, Vaskülit

A case of juvenil dermatomyositis

Juvenile dermatomyositis (JDM), the most common of the pediatric inflammatory myopathies, is a systemic vasculopathy with characteristic cutaneous findings and focal areas of myositis resulting in progressive proximal muscle weakness that is responsive to the prompt institution of immunosuppressive therapy. JDM is mostly seen between the ages of 5-14 years of age. Since our case was 16 months, we wanted to consider that JDM may be seen at smaller ages, too.

Keywords:

Dermatomyositis, Muscular Diseases, Vasculitis,

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