Sedat Özcan, Tolga Kurt, Selim Ekinci, Murat Civan, Murat Ziyrek, Hüseyin Toman

Ender bir olgu: Yeniden açılan foramen ovale nedeniyle sağdan sola şanta yol açan orta düzeyde gradyanlı pulmoner supravalvuler stenoz

Sağdan sola şantın eşlik ettiği supravalvuler pulmoner stenoz erişkinlerde ender görülen bir ekokardiyografi bulgusudur. Önceden tanısı konmamış patent foramen ovaleden gelişen sağdan sola şantın eşlik ettiği supravalvuler pulmoner stenoz gelişen hastanın olgusu sunulmuştur. Bu konjenital anomali, valvuler pulmoner stenozdan tedavi yöntemlerinin ayrı olmasından dolayı ayırıcı tanısı yapılmalıdır.

Anahtar Kelimeler:

Pulmoner, supervalvular stenoz, foramen ovale

A rare case: Pulmonary supravalvular stenosis with moderate gradient causing an atrial right to left shunt across the reopened foramen ovale

Supravalvular pulmonary stenosis accompanied by a right to left shunt is a rare echocardiographic finding in adults. We report a case of adult pulmonary supravalvular membranous stenosis with an atrial right to left shunt developed through a previously undiagnosed patent foramen ovale (PFO).The peculiarity of our case is that foramen ovale reopened despite a moderate pulmonary trunk gradient over a six year period. This congenital anomaly is a condition to be differentiated from valvular pulmonary stenosis as both anomalies require different modalities of treatment (surgical or catheter).

Keywords:

Pulmonary, supervalvular stenosis, foramen ovale,

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1. Kodama K, Owa M, Saito M, et al: A case of adult pulmonary suprvalvular membranous stenosis which was successfully treated by percutaneous transluminal balloon dilatation. To Junkan 1992;40:1025–1029.
2. Maffee et al.,Isolated Supravalvular Pulmonary Stenosis: A Rare Echocardiographic Finding Echocardiography 2014;31:E215–E217
3. Oster ME, Riehle-Colarusso T, Correa A: An update on cardiovascular malformations in congenital rubella syndrome. Defects Res A Clin Mol Teratol 2010;88:1–8.
4. Habash S, Haas NA, Laser KT: Interventional therapy of supravalvular pulmonary stenosis via a mechanical valve in the pulmonary position. Heart Dis 2014;8:E41–45.
5. Delmo Walter EM, Miera O, Nasseri B, et al: Onset of pulmonary stenosis after arterial switch operation for transposition of great arteries with intact ventricular septum. Proc Intensive Care Cardiovasc Anesth 2011;3:177–187
6. Kuroczynski W, Kampmann C, Choi YH, Hilker M, Wippermann F, David M, Schmid FX, Heinemann MK, Oelert H.Treatment of supravalvular pulmonary stenosis after arterial switch operations,hyperlink "http://www.ncbi.nlm.nih.gov/pubmed/11515280" Z Kardiol. 2001 Jul;90(7):498-502
7. Gökçeer T, Yaylacı A, Akkaynak AÇ, Peker Ö, Karaaslan O. Nasal schwannoma: a report of two cases. Kulak Burun Bogaz Ihtis Derg 2004;13:46-50.
8. Hasegawa SL, Mentzel T, Fletcher CD. Schwannomas of the sinonasal tract and nasopharynx. Mod Pathol 1997;10:777-784.
9. Siqueira MG, Jennings E, Moraes OJS ve ark. Nasoethmoid schwannoma with intracranial extension. Arg Neuropsiquiatr 2001;59:421-423. 10. Coakham HB. Nasoethmoid schwannoma with intracranial extension. Case report and review of literature. Br J Neurosurg 2009;23:636.