Berna AYTAÇ VURUŞKAN, Sevda AKYOL, Hakan VURUŞKAN

Kistik Nefromalı Olguların Klinikopatolojik Özellikleri: Olgu Serisi

Kistik nefroma böbreğin nadir görülen multikistik benign tümörüdür. Çalışmamızda 2005– 2017 yılları arasında, Kistik Nefroma tanısı almış 20 olgu, retrospektif olarak incelenerek, klinik ve histopatolojik özellikleri ortaya konuldu. Hasta kayıtlarından elde edilen bilgiler, klinik hikâyeleri, klinik tanısı ve cerrahi materyalin histopatolojik özelliklerine göre not edildi. Olguların 15’ i kadındı. Yaş aralığı 1 - 63 arasındaydı. 12 vakada lomber veya yan ağrısı şikayeti mevcuttu. 14 hastaya radikal, 6 hastaya parsiyel nefrektomi yapıldı. Olguların takiplerinde rekürrens görülmedi. Kistik nefromalar klinik ve radyolojik olarak diğer kistik renal tümörlerle karışabilir, ayırıcı tanıda histopatolojik inceleme gereklidir.

Anahtar Kelimeler:

Kistik nefroma, böbrek, erişkin, pediatrik

Clinicopathologic Features of Cystic Nephroma: Series of Cases

Cystic nephroma is a rare multicystic benign tumor of kidney. In our study we evaluated retrospectively the clinical and histopathologic features of 20 patients with cystic nephroma that were diagnosed between 2005-2017. Demographics of patients, clinical history, clinical diagnosis and pathologic characteristics of the specimen were assessed. 15 patients were female. Ages ranged from 1 to 63 years. 12 patients had lomber or flank pain. 14 patients underwent radical and 6 patients underwent partial nephrectomy. There was no recurrence during follow-up. Cystic nephromas mimic other cystic renal neoplasms clinically and radiologically, necessitating histopathological examination for definitive diagnosis.

Keywords:

Cystic nephroma, kidney, adult, pediatric,

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