Gonca YILMAZ, Çiğdem ÜNER, Sevgi DURMUŞ YAŞAR

Şüpheli cilt bulgusu saptanan çocuklarda okült spinal disrafzm sıklığı: Geriye dönük bir çalışma

Amaç: Hastanemize şüpheli cilt bulgusu yakınmasıyla başvuran ve rutin muayene sırasında cilt bulguları saptananolgularda okült spinal disrafzm sıklığının saptanması ve sonuçların literatürle kıyaslanmasıdır.Gereç ve Yöntemler: Dr. Sami Ulus Kadın Doğum ve Çocuk Sağlığı ve Hastalıkları Hastanesine Haziran 2012 veHaziran 2013 tarihleri arasında başvuran ve şüpheli cilt bulguları olan olgular geriye dönük olarak incelendi.bulgular: Şüpheli cilt bulgusu saptanan 117 olgu çalışmaya dahil edildi. En sık cilt bulgusu 102 olguda saptanan sakralgamze (%87)di. Diğer bulgular; 7 olguda kıllanma artışı (%6), 5 olguda sakral gamze ve kıllanma artışı birlikteliği (%4),2 olguda sakral sinüs (%2), 1 olguda sakral kitle (%1)di. Değerlendirilen tüm olguların %7 sinde okült spinal disrafzmsaptandı.sonuç: Okült spinal disrafzmin erken tanısında cilt bulguları önemli bir yer tutmaktadır. Bu nedenle özellikle yenidoğanmuayenelerinde klinisyenin dikkatli olması gerekmektedir. Cilt bulguları saptanan çocuklarda görüntüleme yöntemleriakılcı bir şekilde kullanılmalıdır.

The frequency of occult spinal dysraphism in children with suspicious skin findings: A retrospective study

Objective: The aim of this study was to determine the incidence of occult spinal dysraphism in patients complainingabout skin fndings and those with skin signs determined during routine medical examination and to compare the resultswith the literature.Material and Methods: Patients presenting to the Dr. Sami Ulus Obstetrics and Gynecology, Children Health andDisease Training and Research Hospital between July 2012 and July 2013 and found to have suspicious skin fndingswere evaluated retrospectively.Results: We included 117 cases with suspicious skin fndings in this study. The most frequent skin fnding was a sacraldimple (87%) that was found in 102 cases. The other fndings were hypertrichosis (6%) in 7 cases, coexistence of sacraldimple and hypertrichosis (4%) in 5 cases, sacral sinus (2%) in 2 cases and sacral mass (1%) in 1 case. Occult spinaldysraphism was found in 7% of all evaluated cases.conclusion: Skin signs have an important role in the early diagnosis of occult spinal dysraphism. Clinicians shouldtherefore be careful during examinations and especially newborn examinations. Imaging methods must be used wisely forchildren when skin signs are found.

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