Sevgi Yaşar DURMUŞ, Çiğdem ÜNER, Gonca YILMAZ

Şüpheli Cilt Bulgusu Saptanan Çocuklarda Okült Spinal Disrafizm Sıklığı: Geriye Dönük Bir Çalışma

Amaç: Hastanemize şüpheli cilt bulgusu yakınmasıyla başvuran ve rutin muayene sırasında cilt bulguları saptanan olgularda okült spinal disrafizm sıklığının saptanması ve sonuçların literatürle kıyaslanmasıdır.Gereç ve Yöntemler: Dr. Sami Ulus Kadın Doğum ve Çocuk Sağlığı ve Hastalıkları Hastanesine Haziran 2012 ve Haziran 2013 tarihleri arasında başvuran ve şüpheli cilt bulguları olan olgular geriye dönük olarak incelendi.Bulgular: Şüpheli cilt bulgusu saptanan 117 olgu çalışmaya dahil edildi. En sık cilt bulgusu 102 olguda saptanan sakral gamze (%87)’di. Diğer bulgular; 7 olguda kıllanma artışı (%6), 5 olguda sakral gamze ve kıllanma artışı birlikteliği (%4), 2 olguda sakral sinüs (%2), 1 olguda sakral kitle (%1)’di. Değerlendirilen tüm olguların %7 sinde okült spinal disrafizm saptandı.Sonuç: Okült spinal disrafizmin erken tanısında cilt bulguları önemli bir yer tutmaktadır. Bu nedenle özellikle yenidoğan muayenelerinde klinisyenin dikkatli olması gerekmektedir. Cilt bulguları saptanan çocuklarda görüntüleme yöntemleri akılcı bir şekilde kullanılmalıdır.

Anahtar Kelimeler:

Cilt, Okült spinal disrafizm

Suspicious Skin Findings: A Retrospective Study The Frequency of Occult Spinal Dysraphism in Children with

Objective: The aim of this study was to determine the incidence of occult spinal dysraphism in patients complaining about skin findings and those with skin signs determined during routine medical examination and to compare the results with the literature.Material and Methods: Patients presenting to the Dr. Sami Ulus Obstetrics and Gynecology, Children Health and Disease Training and Research Hospital between July 2012 and July 2013 and found to have suspicious skin findings were evaluated retrospectively.Results: We included 117 cases with suspicious skin findings in this study. The most frequent skin finding was a sacral dimple (87%) that was found in 102 cases. The other findings were hypertrichosis (6%) in 7 cases, coexistence of sacral dimple and hypertrichosis (4%) in 5 cases, sacral sinus (2%) in 2 cases and sacral mass (1%) in 1 case. Occult spinal dysraphism was found in 7% of all evaluated cases.conclusion: Skin signs have an important role in the early diagnosis of occult spinal dysraphism. Clinicians should therefore be careful during examinations and especially newborn examinations. Imaging methods must be used wisely for children when skin signs are found

Keywords:

Skin, Occult spinal dysraphism,

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