Esra KARAKUŞ, Bahattin TUNÇ, Suna EMİR, Derya ÖZYÖRÜK, Hacı Ahmet DEMİR, Cengiz BAYRAM

Çocuklarda Primer Kutanoz T- Hücreli Lenfoma: İki Olgu Sunumu

Primer kutanöz lenfomalar çocukluk çağında çok nadir olup histolojik alt tip, klinik seyir ve prognoz bakımından farklılık gösterirler. Burada farklı histopatolojik özelliklere sahip iki primer kutanöz lenfoma olgusu sunulmaktadır. Her iki olgunun ortak özelliği sistemik antibiyotik ve pansuman tedavilerine yanıt vermeyen cilt apsesi ile başvurmuş olmalarıydı. Biyopsi ve evreleme çalışmalarından sonra bir olgu primer kutanöz periferik T hücreli lenfoma, tanımlanamayan, diğer olgu ise primer kutanöz CD30 pozitif ALK negatif anaplastik büyük hücreli lenfoma tanısı aldı.

Anahtar Kelimeler:

Kutanöz anaplastik büyük hücreli lenfoma, Periferik T hücreli lenfoma, Primer kutanöz lenfoma

Primary Cutaneous T-Cell Lymphoma in Children: Report of Two Cases

Primary cutaneous lymphomas in children are rare and constitute a heterogeneous group in regard to histological subtype, clinical course and prognosis. Here, we present the clinical characteristics and outcomes of two children with primary cutaneous lymphoma with different histopathologic subtypes. They had been diagnosed as a skin abscess initially but had not responded to systemic antibiotherapy and dressing. After a biopsy and metastatic work up, one patient was diagnosed as primary cutaneous peripheral T-cell lymphoma, unspecified, and the other as primary cutaneous CD30 positive ALK negative anaplastic large cell lymphoma

Keywords:

Cutaneous anaplastic large cell lymphoma, Peripheral T-cell lymphoma, Primary cutaneous lymphoma,

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