Tuğba Şişmanlar EYÜBOĞLU, Ayşe Tana ASLAN, Deniz Gezgin YILDIRIM, Necla BUYAN, Serhat EMEKSİZ, Gökhan KALKAN

What triggered massive hemoptysis in Goodpasture syndrome with isolated pulmonary involvement in a 14-year-old boy?

Goodpasture syndrome is a rare, autoimmune disease associated with thedevelopment of antibodies against a specific antigen both in glomerularbasement membrane and alveolar basement membrane. It is very rarein childhood and its incidence is not known. Although the mechanismof the disease is the same in lung as in the kidney, sometimes it presentswith involvement of only one organ. Pulmonary involvement may be lifethreatening in patients with massive hemoptysis. Herein we report a 14-yearold boy with isolated lung involvement. He had massive hemoptysis followingbronchoscopy and recovered succesfully with treatment.

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