An infant with intradural extramedullary synovial sarcoma: the youngest case in the literature

An infant with intradural extramedullary synovial sarcoma: the youngest case in the literature

Spinal cord involvement of synovial sarcoma is extremely rare. So far onlytwo cases have been reported. Herein we describe the youngest case in theliterature. She is 14-month-old and first presented with difficulty in walkingongoing for a week. Imagining showed a spinal cord mass at C5-T3 levels.The patient had gone under Decompressive surgery and histopathologicexamination of the specimen revealed the presence of synovial sarcoma.Although the tumor regressed after chemotherapy, she was lost due to viralpneumonia. Synovial sarcoma should be kept in mind while evaluating spinaltumors even in infantile group.

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Turkish Journal of Pediatrics-Cover
  • ISSN: 0041-4301
  • Yayın Aralığı: Yılda 6 Sayı
  • Başlangıç: 1958
  • Yayıncı: Hacettepe Üniversitesi Çocuk Sağlığı Enstitüsü Müdürlüğü
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