Kuddusi TEBERİK, Bayazıt İLHAN, Sibel POLAT, Çiğdem Ülkü CAN, Orhan ZİLELİOĞLU

Surgical management of anterior lenticonus in a patient with Alport’s syndrome

Amaç: Alport sendromlu bir hastada oftalmik bulguları ve ön lentikonusun tedavisini tartışmak. Materyal ve Metod: Alport sendromlu 22 yaşındaki bayan hastada oftalmik bulgu olarak bilateral ön lentikonus mevcuttu. Sağ gözüne başka bir klinikte yüksek miyopi nedeniyle laser in situ keratomileusis (LASIK) uygulanmış olan hastanın diğer gözüne kliniğimizde fakoemülsifikasyon ve katlanabilir intraoküler lens implantasyonu yapıldı. Bulgular: Fakoemulsifikasyon ile lens ekstraksiyonu ve intraoküler lens implantasyonu ile iyi bir görsel sonuca ulaşılmıştır. Daha önce LASIK uygulanmış diğer göz yumuşak kontakt lens ile rehabilite edilmiştir. Sonuç: Ön ve arka lentikonus kolaylıkla gözden kaçabileceğinden refraktif cerrahi uygulanacak olgularda ameliyat öncesinde hastanın çok dikkatli muayene edilmesi şarttır. Lentikonusun tedavisi lens ekstraksiyonu ve intraoküler lens implantasyonu olmalıdır.

Alport sendromlu bir hastada ön lentikonusun cerrahi tedavisi

Background: To discuss ophthalmic features and management of a patient with Alport’s syndrome and anterior lenticonus. Materials and Methods: A 22-year-old female patient with Alport’s syndrome who, in another center, had undergone laser in situ keratomileusis (LASIK) because of high myopia was determined to have bilateral anterior lenticonus. We treated the other eye by phacoemulsification and intraocular lens (IOL) implantation. Results: Lens extraction and IOL implantation gave satisfactory results. The eye undergone LASIK was rehabilitated by a contact lens. Conclusion: As anterior and/or posterior lenticonus is easily overlooked, careful evaluation of patients with high refractive errors is essential before any decision for refractive surgery. Treatment of lenticonus should be by lens extraction and IOL implantation.

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