Nur AYDINLI, Mine ÇALIŞKAN, Ahmet YARAMIŞ, Burak TATLI, Meral ÖZMEN, Bülent KARA, Ceren YILMAZ, Kubilay AYDIN

Erken basınçlı multipl skleroz

Multipl skleroz merkezi sinir sisteminde farklı demiyelinizasyon ve aksonal hasar alanlarıyla belirgin, kronik bir hastalıktır. Olguların %2-5'inde hastalık 16 yaşından önce başlar. Çocuklarda arka çukur plakları ve "tümefaktif' lezyonlar daha sıktır. Bir yıl önce akut dissemine ansefalomiyelit tanısı alan ve ikinci atağında tümör ve apse ile karıştırılan "tümefaktif' lezyonları olan 14 yaşındaki erkek olguya multipl skleroz tanısı kondu. Multipl skleroz'un çocukluk döneminde tanı, ayırıcı tanı ve tedavisinin tartışılması amaçlandı.

Early onset multipl sclerosis

Multipl sclerosis is a chronic disease of the central nervous system, characterized by discrete areas of demyelination and axon injury. "The occurrence of multipl sclerosis in children younger than 16 years has been found to between 2-5%. The incidence of posterior fossa plaques and tumefactive lesions were higher in children. A fourteen-year old boy who had a history of acute disseminhated encsephalomyelitis one year before and demosttrated tumefactive plaques confused with tumor or abscess, in the second attack was diagnosed as multipl sclerosis. Current knowledge of the diagnosis, differential diagnosis and therapy of multipl sclerosis are discussed.

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