Ayşe YILDIRIM, Ayla AKÇA, F. Sedef TUNAOĞLU

Atriyal flattere neden olan hamak mitral kapak: Üç aylık bebek olgu

Hamak mitral kapak oldukça nadir görülen doğuştan mitral kapak hastalığıdır. Çocuklarda mitral darlık ya da yetersizliğe neden olabilir. Hastalar sıklıkla kliniğe kalp yetersizliği bulguları ile gelirler, ancak ani ölüm de görülebilmektedir. Kliniğimize kalp yetersizliği bulguları ile başvuran üç aylık kız bebeğe yapılan incelemeler sonucunda; hamak mitral kapak, sol atriyal genişleme, önemli mitral kapak yetersizliği ve atriyal flatter tanıları koyuldu. Erişkinlerin aksine, bu yaş grubunda atriyal flatter çok nadir görülen bir aritmidir. Bu olguyu hamak mitral kapağa bağlı gelişen atriyal flatter olgusunun daha önce sunulmamış olması nedeni ile sunduk.

Hammock mitral valve as a cause of atrial flutter: Three months old infant case

Hammock mitral valve is a very rare congenital valve disorder. It may lead to mitral stenosis or insufficiency in the pediatric age group. These patients generally present with the symptoms of congestive heart failure or sometimes sudden death may occur. Our case was a three-month-old female infant who presented to our clinic with the symptoms of heart failure. Her cardiac evaluation revealed hammock mitral valve, left atrial dilatation, severe mitral valve insufficiency and atrial flutter. In contrast to adult patients, atrial flutter is a very rare type of cardiac aryhtmia in the pediatric age group. We present this case, because no such a case with atrial flutter resulting from hammock mitral valve has been reported in the literature.

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