Cem ÇOMUNOĞLU, Özlem ÖNEN, Kübra BOYNUKALIN, Cem BAYKAL, Ali AYHAN

TUBANIN MALİGN MİKST MÜLLERİAN TÜMÖRÜ: MORFOLOJİK AÇIDAN FARKLI İKİ OLGU

Amaç: Malign mikst müllerian tümörler (MMMT) epitelyal ve mezenkimal komponentler içeren çok agresif bifazik neoplazmlardır. Kadın genital sisteminde tubada MMMT’ler nadiren görülürler. Olgu Sunumu: Bu bildiride tuba fimbrial uç yerleşimli iki MMMT olgusu sunulmaktadır. Her iki hastada FIGO evresi IIIC (T3c N0 M0) idi. Tümörlerden biri homolog, diğeri heterolog tipteydi. Tartışma: Bu nadir tümörlerin prognozu kötüdür. Hastalarımızdan biri tanı konduktan 6 ay sonra yaşamını yitirmiştir. Bu tümörler için sağkalımı artırmada tam cerrahi, kemoterapi ve eksternal radyoterapi zorunlu görünmektedir.

Anahtar Kelimeler:

Karsinosarkom, malign mikst müllerian tumor, tuba.

MALIGNANT MIXED MÜLLERIAN TUMOR OF THE FALLOPIAN TUBE: MORPHOLOGICALLY DIFFERENT TWO CASES

Objective: Malignant mixed müllerian tumors (MMMT) are highly aggressive biphasic neoplasms consisting of both epithelial and mesenchymal components. In female genital tract, MMMTs are rarely seen in fallopian tube. Case Report: We will present two cases of MMMT of fallopian tube located at the fimbrial end. Both patients were FIGO stage IIIC (T3c N0 M0). One of the tumor was homologous and the other one heterologous variety. Conclusion: These rare tumors have poor prognosis, as one of the patients died only in 6 months after the diagnosis. For these tumors complete surgery, chemotherapy and external radiation seemed to be necessary in order to improve survival.

Keywords:

Carcinosarcoma, malignant mixed müllerian tumor, Fallopian tube,

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