Ercan GÜRSES, Vefa ÖZCAN, Harun EVRENGÜL, Ahmet BALTALARLI, İbrahim GÖKŞİN, Mustafa SAÇAR

Siyanoz ve senkop ile başvuran 16 yaşındaki hastada Ebstein anomalisi

Ebstein anomalisi triküspid kapağın nadir bir malformasyonudur; tüm doğuştan kalp hastalıklarının %0.5'ini oluşturur. Kliniğimize siyanoz ve senkop yakınması ile başvuran 16 yaşında bir erkek hastada tip B Ebstein anomalisi saptandı. Hasta, Carpentier tipi onarım tekniği kullanılarak başarılı şekilde ameliyat edildi. Ameliyattan hemen sonra siyanoz tümüyle kayboldu. Hastanın ameliyat sonrası iyileşmesi sorunsuz gerçekleşti.

Ebstein's anomaly in a 16-year-old child presenting with cyanosis and syncope

Ebstein's anomaly is an uncommon malformation of the tricuspid valve, accounting for 0.5% of all congenital heart diseases. We presented a 16-year-old male child with type B Ebstein's anomaly, who presented with complaints of cyanosis and syncope. He was successfully operated on with the Carpentier's repair technique. Cyanosis completely disappeared just after the operation and the patient had an uneventful recovery period.

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