Ömer Faruk DEMİR, Ömer ÖNAL, Leyla HASDIRAZ, Fahri OĞUZKAYA, Ayşe ÜLGEY, Olgun KONTAŞ

Plöropulmoner blastom: İki olgu sunumu

Plöropulmoner blastom çocukluk çağında mezenkimal kökenli, nadir ve agresif bir tümördür. Prognozu kötü olup, başlıca kistik (tip 1), mikst tip (tip 2) ve solid (tip 3) olarak sınıflandırılır. Bu yazıda plöropulmoner blastomun nadir bir klinik tablosu olan pnömotoraksın eşlik ettiği ve cerrahi ile başarılı bir şekilde tedavi edilen iki plöropulmoner blastom tip 3 olgusu sunuldu.

Pleuropulmonary blastoma: A report of two cases

Pleuropulmonary blastoma is a rare and aggressive childhoodtumor of mesenchymal origin. It has a poor prognosis andmainly classified as cystic (type 1), mixed type (type 2), andsolid (type 3). Herein, we present two cases of pleuropulmonaryblastoma type 3 presenting with pneumothorax, a rare clinicalpresentation of pleuropulmonary blastoma, which wassuccessfully treated with surgery.

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