Erkan YILMAZ, Baran UĞURLU, Metin MANİSALI, Richard WHİTE

Hipertrofik obstrüktif kardiyomyopatiler: MR ile değerlendirme

Hipertrofik obstrüktif kardiomyopati, kardiyak veya sistemik hastalık olmaksızın sol ventrikülün dilatasyon göstermeyen hipertrofisidir. HOCM'lu 12 hastada MR incelemesinde; ortalama myokardiyal kalınlık bazal septumda 23.5 mm, posterolateral duvarda 16.8 mm ve septumun posterolateral duvara oranı 1.39 olarak saptandı. Bu değerler literatürde kabul gören değerlerle karşılaştırıldı. HOCM'lu hastalarda, ileri obstrüksiyon ile end-diastolik septum duvar kalınlığındaki artış, MR bulguları arasında belirgin ilişki izlendi. Mitral kapağın sistolde öne hareketi, SPAMM tekniğinde grid paternindeki fokal distorsiyon ve sistolde sol ventriküler çıkışta sinyal kaybı gibi.

Hypertrophic obstructive cardiomyopathies: Evaluation with MR

Hypertrophic obstructive (HOCM) cardiomyopathy is a nondilated hypertrophy of the left ventricle in the absence of cardiac or systemic disease that could produce left ventricular hypertrophy. MR imaging was performed in 12 patients with HOCM. The mean myocardial thickness was 23.5 mm in the basal septum, 16.8 mm in the posterolateral wall and the ratio of septal to posterolateral wall thickness was 1.39. These values were compared with accepted normals in the literature. In patiens with HOCM, gross correlation was demostrated between severity of obstruction and MR features, including increased end - diastolic thickness of the septal wall, systolic anterior motion of the mitral value, focal distortion of grid pattern in SPAMM techniques and signal void the left venticular outflow treat during systole.

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