Murat GÜVENER, Orhan Saim DEMİRTÜRK, Mediha Hacer ÜlGER, Ayten GÜMÜŞ

An absent right superior vena cava with a persistent left superior vena cava combined with the presence of a ventricular septal defect in a pediatric patient: Implications for surgical correction

Kalıcı sol superior vena kava, sağ superior vena kavanın yokluğu ile birlikte, venöz dolaşımın çok nadir rastlanan bir anomalisidir. Bu yazıda genişlemiş bir koroner sinüse açılan persistan sol superior vena kava ve kardiyopulmoner baypas cerrahisi ile düzelttiğimiz perimembranöz bir çıkım yolu ventriküler septal defekti eşliğinde görülen sağ superior vena kava yokluğunun olduğu dört yaşındaki bir kız olgu sunuldu.

Pediatrik bir hastada ventriküler septal defekt varlığında persistan sol superior vena kava eşliğinde sağ superior vena kava yokluğu: Düzeltme cerrahisi için öneriler

A persistent left superior vena cava in conjunction with a absent right superior vena cava is a very rare anomaly of venous circulation. In this article, we present a fouryear- old girl with a persistent left superior vena cava opening into a dilated coronary sinus and an absent right superior vena cava accompanied by a perimembraneous outlet ventricular septal defect which were corrected using cardiopulmonary bypass surgery.

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