Birgül VARAN, Şule AKÇAY, Şerife BOZBAŞ SAVAŞ

Sağ pulmoner ven atrezisi: Olgu sunumu ve literatürün gözden geçirilmesi

Eşlik eden doğumsal bir patoloji olmaksızın izole pulmoner ven atrezisi erişkinlerde oldukça nadir görülmektedir, artmış mortalite ve morbidite ile ilişkilidir. Hastalar tekrarlayan akciğer infeksiyonları, eforla gelişen nefes darlığı ve hemoptizi şi- kayetleriyle hastaneye başvurmaktadırlar. Çok nadir görülmesi nedeniyle tanı ve tedavide birtakım zorluklar yaşanabil- mektedir. Bu yazıda, erişkin yaşta saptanan izole pulmoner ven atrezili olgu nedeniyle tanı ve tedavi seçenekleri gözden geçirilmiştir.

Right pulmonary venous atresia: a case report and review of literature

Isolated pulmonary vein atresia without associated congenital malformation is a very rare condition in adults. It is associ- ated with significant mortality and morbidity. Recurrent pulmonary infections, dyspnea on exertion and hemoptysis may be the presenting complaints. Owing to the limited number of patients with this condition there may be some difficulties in it’s diagnosis and therapy. We report an adult case with this rare congenital malformation and discuss it’s diagnosis and management options.

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