Akın KAYA, Bülent Mustafa YENİGÜN, Cabir YÜKSEL, Gökhan ÇELİK, Hakan KUTLAY, Levent YAZICIOĞLU, Aydın ÇİLEDAĞ, Sibel PERÇİNEL

Pulmonary artery sarcoma mimicking pulmonary thromboembolism

Otuz yaşında erkek hasta, toraks bilgisayarlı tomografi (BT) anjiyografide sol ana pulmoner arterde lümeni tam tıkayan trombüs saptanması üzerine pulmoner emboli tanısı ile hastanemize refere edildi. Kliniğimizde, lezyon tümöral kitle olarak değerlendirildi. Pozitron emisyon tomografi (PET)-BT'de, pulmoner arterdeki kitlede patolojik tutulum saptandı. Tümörün lokalizasyonu nedeniyle sol pnömonektomi uygulandı. Patolojik incelemede pulmoner arter sarkomu saptandı. Olgu, pulmoner arter sarkomunun nadir görülmesi ve pulmoner emboliyi taklit edebilmesi nedeniyle sunuldu. Pulmoner arter sarkomunun gerçek prevalansı, birçoğunun yanlışlıkla pulmoner tromboemboli tanısı alması nedeniyle tahmin edilenin üzerindedir. PET-BT ayırıcı tanıda yardımcı olabilir.

Pulmoner tromboemboliyi taklit eden pulmoner arter sarkomu

A 30 years old male patient was referred to our hospital with a diagnosis of pulmonary thromboembolism due to thorax-computerized tomography (CT) angiography, revealing a thrombus totally occluding left main pulmonary artery. The lesion was evaluated as tumoural mass. Positron emission tomography (PET)-CT revealed pathologic uptake at pulmonay artery mass. Due to localization of tumour, left pneumonectomy was performed. The pathological diagnosis revealed to be pulmonary artery sarcoma. The patient was presented because pulmonary artery sarcomas are very rare tumors and can mimick pulmonary thromboembolism. The true prevalence is underestimated as many pulmonary artery sarcomas are misdiagnosed as pulmonary thromboembolism. PET-CT may help to make a differential diagnosis.

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