Murat BİÇER, Cengiz GEBİTEKİN, Sami Ahmet BAYRAM

Extrapulmonary sequestration mimicking mediastinal cyst: Report of two identical cases

Ekstrapulmoner sekestrasyon nadir olarak görülen ve genellikle yaşamın ilk altı ayında ortaya çıkan konjenital anomalidir. Sıklıkla sol akciğer alt lobu ile diyafragma arasında yer alır. Mediastinal yerleşim nadirdir. Biz bu yazımızda rastlantısal olarak tespit ettiğimiz ekstrapulmoner sekestrasyonlu iki erkek çocuk olgumuzu tanımladık. Bu tanı; anterior mediastinal kitleli tüm çocuklarda akılda tutulmalıdır.

Mediastinal kist gibi davranan ekstrapulmoner sekestrasyonlu iki olgu

Extrapulmonary sequestration (EPS) is a rare congenital anomaly usually diagnosed during the first six months of life. It is mostly found between the left lower lobe of the lung and the diaphragm. Mediastinal presentation is extremely rare. We describe two identical cases of extrapulmonary sequestration mimicking mediastinal cystic mass in two boys. These emphasize the need to keep this diagnosis in mind when dealing with children presenting with anterior mediastinal mass.

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1. Felker RE, Tonkin ILD. Imaging of pulmonary sequestration. Am J Roentgenol 1990; 23: 220-3.
2. Savic B, Birtel FJ, Tholen W, et al. Lung sequestration: Report of seven cases. Thorax 1979; 34: 96-101.
3. Lupinski RW, Agasthian T, Lim CH, et al. Extrapulmonary sequestration simulates posterior neurogenic tumor. Ann Thoracic Surg 2004; 77: 2203-4.
4. Gamillscheg A, Beitzke A, Smolle-Jütnerr FM, et al. Extralobar sequestration with unusual arterial supply and venous drainage. Pediatr Cardiol 1996; 17: 57-9.
5. Stocker JT. Sequestration of the lung. Semin Diagn Pathol 1986; 3: 106-21.
6. Kim KW, Kim WS, Cheon JE, et al. Complex bronchopulmonary foregut malformation: Extralobar pulmonary sequestration associated with a duplication cyst of mixed bronchogenic and oesophageal type. Pediatr Radiol 2001; 31: 265-8.
7. Flye MW, Conely M, Silver D. Spectrum of pulmonary sequestration. Ann Thorac Surg 1976; 22: 478-82.
8. John PR, Beasley SW, Mayne V. Pulmonary sequestration and related congenital disorders. A clinico-radiological review of 41 cases. Pediatr Radiol 1989; 20: 4-9.
9. Schwartz MZ, Ramachandran P. Congenital malformations of the lung mediastinum-A quarter century of experience from a single institution. J Pediatr Surg 1997; 32: 44-7.
10. Clements BS, Warner J, Shinebourne EA. Congenital bronchopulmonary vascular malformation: Clinical application of a simple approach in 25 cases. Thorax 1987; 42: 402-16.