Figen ATALAY, Dilek ERNAM, Aysun ALP, H. Canan HASANOĞLU

A Behçet’s disease patient with intracardiac thrombus, pulmonary artery aneurysms complicating recurrent pulmonary thromboembolism

İntrakardiyak trombüs, pulmoner arter anevrizması ve pulmoner tromboemboli Behçet hastalığının nadir görülen bulgularındandır. Yirmi yaşında erkek hasta nefes darlığı, hemoptizi, ateş ve görmede bulanıklık yakınmaları ile başvurdu. Dinamik toraks bilgisayarlı tomografi (BT)’de bilateral pulmoner arter segmentlerinde anevrizmatik dilatasyon, trombüsle birlikte her iki alt lobda pulmoner emboli ile uyumlu kollaps-konsolidasyon alanları izlendi. Klinik ve radyolojik bulgular birarada değerlendirildiğinde Behçet hastalığı tanısı kondu. Hasta tedavi altındayken tekrarlayan pulmoner tromboemboli nedeniyle iki kez hospitalize edildi. Kontrol dinamik toraks BT’de pulmoner arter anevrizmatik dilatasyonlarda ve trombüslerde kısmi gerileme izlenirken, sağ ventrikülde trombüs saptandı. Hasta halen tedavi altında olup semptomu yoktur. Biz olgumuzu, Behçet hastalığında tekrarlayan pulmoner tromboembolinin nadir görülmesi ve tedavi altında iken intrakardiyak trombüs gelişimi nedeniyle sunuyoruz.

Tekrarlayan pulmoner tromboemboli ile komplike pulmoner arter anevrizması ve intrakardiyak trombüs ile seyreden Behçet hastalığı olgusu

Intracardiac thrombus and pulmonary embolism is a very rare manifestation of Behçet’s disease. A twenty-years-old man was admitted to hospital due to dyspnea, haemoptysis, fever and partially loss of vision. On dynamic thorax computed tomography (CT), there was aneurysmatic dilatation and thrombus in bilateral pulmonary artery segments and also findings of pulmonary thromboembolism. A diagnosis of Behçet’s disease was made based on his clinical course and radiological findings. During treatment, the patient was admitted two times to the hospital because of recurrent pulmonary thromboembolism. At the 10th months of follow up, partially dissolution of the thrombi and pulmonary defects were observed and right ventricular thrombus was revealed by dynamic thorax CT. On a follow up period of 16 months the patient is still under treatment and doing well. We present this case because Behçet’s disease is a rarely considered cause of recurrent pulmonary embolism and intracardiac thrombus which is seen under treatment.

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