AYSUN ŞİKAR AKTÜRK, Rebiay KIRAN, Kaçar Sevgiye ÖZKARA, Gökhan BÜYÜKKALE

Neonatal bullous urticaria pigmentosa: Case report

Mastositoz, mast hücrelerinin deri ve diğer organlarda anormal infiltrasyonu ile karakterize heterojen bir grup hastalıktır. Kutanöz mastositozun çocuklarda en yaygın formu ürtikerya pigmentozadır. Büllöz mastositoz terimi, belirgin özelliği bül olan mastositozlu olguları tanımlamak için kullanılır. Bu tipte sistemik tutulum daha sıktır. Tipik lezyonlar ve semptomlar yoksa büllöz mastositoz tanısını koymak her zaman mümkün olmaz ve büllöz impetigo, primer herpes simpleks virus enfeksiyonu, immüno-büllöz hastalıklar, neonatal lupus, incontinentia pigmenti ve eritema multiforme gibi diğer büllöz hastalıklar ile karışabilir. Mastositoz tanısı genellikle klinik ve histopatolojik inceleme ile konur. Ek olarak, Tzanck smear gibi basit bir teknikle hızlı olarak teşhis edilebilir. Burada Tzanck smear ile hızlı bir şekilde tanı konan, büllöz ürtikerya pigmentozalı 20 günlük bir erkek çocuk bildirilmektedir.

Neonatal büllöz ürtikerya pigmentoza: Olgu sunumu

Mastocytosis is a heterogeneous group of diseases characterized by the abnormal infiltration of mast cells in the skin and other organs. The most common type of cutaneous mastocytosis in children is urticaria pigmentosa. The term “bullous mastocytosis” is used to describe cases with mastocytosis in which bullae was a prominent feature. Systemic involvement is more frequent in this type. If typical lesions and symptoms are absent, the diagnosis of bullous mastocytosis is not always evident and other bullous diseases such as bullous impetigo, primary herpes simplex virus infection, immuno-bullous disease, neonatal lupus, incontinentia pigmenti and erythema multiforme could be considered. The mastocytosis is usually diagnosed with clinical and histopathological examination. In addition, the disease was recognized rapidly and promptly by a simple technique such as Tzanck smear. Here, we report a 20-day-old boy with neonatal bullous urticaria pigmentosa that was diagnosed rapidly with Tzanck smear.

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