Palatal miyoklonus

Palatal miyoklonus, son derece nadir görülen bir hastalıktır. Tinnitus yumuşak damağın ritmik istemsiz hareketlerine bağlı olarak oluşur. Klinik tanı dışarıdan duyulabilen kulakta tıklama sesiyle beraber yumu- şak damak hareketlerinin görülmesi ile konur. Bu yazıda, on yıldır kulakta tıklama sesi öyküsü olan ve esansiyel palatal miyoklonus tanısı konulan 38 yaşında bir kadın olgu sunuldu. Hastalık ve semptomatik palatal miyoklonus ile ayırıcı tanısı literatür verileri ışığında değerlendirildi

Anahtar Kelimeler:

Esansiyel palatal miyoklonus, objektif tinnitus, semptomatik palatal miyoklonus

Palatal myoclonus

Palatal myoclonus is an extremely rare disorder. Tinnitus is secondary to rhythmic involuntary movements of the soft palate. Clinical diagnosis is based on the confirmation of the soft palate movements synchronous with an audible clicking noise outside. In this article, we report a 38-year-old female case with a 10 yearhistory of continuing ear click, who was diagnosed with essential palatal myoclonus. The disease and its differential diagnosis from symptomatic palatal myoclonus were discussed in the light of literature data.

Keywords:

Essential palatal myoclonus, objective tinnitus, symptomatic palatal myoclonus,

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