Hakan AVCI, Şenol ÇOMOĞLU, Erkan ÖZTÜRK, Menekşe Bilge BİLGİÇ, Ökkeş Erkan KIYAK

Nazal kondromezenkimal hamartom: Nadir bir nazal benign tümörü

Nazal kondromezenkimal hamartom NKMH nazal kavite ya da paranazal sinüslerden kaynaklanan nadir bir benign burun tümörüdür. Bu yazıda burun tıkanıklığıyla ortaya çıkan ve remisyonda rabdomyosarkom birlikteliği gösteren beş yaşında erkek hasta sunuldu. Plevropulmoner blastom gibi pediatrik tümörlerin eşzamanlı tanısı literatürde dikkate değer bir bulgudur. Hastanın endoskopik muayenesinde sol nazal kavitede septum superior kısmından kaynaklanan ve olfaktör klefte kadar uzanan bir kitle saptandı ve endoskopik cerrahi yaklaşımla tümör tamamen rezeke edildi. Histopatolojik tanıda NKMH’nin kıkırdak ve mezenkimal komponentler içerdiği görüldü. Sonuçta, NKMH pediatrik tek taraflı nazal kitle durumunda ayırıcı tanıda akla gelmesi gereken nadir, plöropulmoner blastom birlikteliği eşzamanlı tanı konabilen ve cerrahi olarak tedavi edilen benign karakterli bir tümördür

Anahtar Kelimeler:

Kondromezenkimal hamartom, tümör, nazal benign tümör

Nasal chondromesenchymal hamartoma: a rare nasal benign tumor

Nasal chondromesenchymal hamartoma NCMH is a rare nasal benign tumor, which arises from the nasal cavity or paranasal sinuses. In this article, we present a five-year-old male patient with rhabdomyosarcoma unity in remission that emerged with nasal obstruction. Synchronous diagnosis of pediatric tumors such as pleuropulmonary blastoma in the literature is a remarkable finding. We found a mass within the left nasal cavity originating from superior portion of nasal septum, extending to the olfactory cleft and resected all tumor via endoscopic surgical approach. Histopathological diagnosis revealed that NCMH contained cartilaginous and mesenchymal components. In conclusion, NCMH is a rare surgically treated benign tumor that can be synchronously diagnosed with pleuropulmonary blastoma and should be kept in mind for differential diagnosis of unilateral pediatric nasal mass.

Keywords:

Chondromesenchymal hamartoma, tumor, nasal benign tumor,

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