Selmin KARADEMİR, Filiz ŞENOCAK, Utku Arman ÖRÜN, Vehbi DOĞAN, Özben CEYLAN, Senem ÖZGÜR, Mahmut KESKİN, Osman YILMAZ

DUCHENNE MUSKÜLER DİSTROFİLİ HASTALARDA SOL VENTRİKÜL FONKSİYONLARININ STRAIN-STRAIN RATE EKOKARDİYOGRAFİ İLE DEĞERLENDİRİLMESİ

Amaç Çalışmamızda konvansiyonel ekokardiyografi ile kalp fonksiyonları normal bulunan Duchenne Musküler Distrofili (DMD) hastaların miyokard fonksiyonlarının pulse wave doku doppler görüntüleme (PWDDG) ve strain/strain rate (S/SR) ekokardiyografi aracılığıyla ölçülmesi ve kontrol grubu ile karşılaştırılması amaçlandı. Gereç ve Yöntem Bu çalışmada; ortalama yaşı 85.2 ± 38.4 ay olan 32 DMD’li erkek hasta ve 89 ± 38.9 ay olan 31 sağlıklı çocuk değerlendirildi. Demografik özellikler olgular ve kontrol grubunda değerlendirildi. Cinsiyet, yaş, vücut kitle indeksi, konvansiyonel ekokardiyografi verileri, pulse wave doku Doppler görüntüleme (PW-TDI) verileri ve iki boyutlu (2D) longitudinal strain (LS) / longitudinal strain rate (LSR) ekokardiyografi değerleri karşılaştırıldı. Bulgular Hasta ve kontrol grupları arasında kalp hızı bakımından istatistiksel olarak anlamlı fark saptandı (p

ASSESSMENT OF LEFT VENTRICULAR FUNCTIONS WITH STRAIN AND STRAIN RATE ECHOCARDIOGRAPHY IN CHILDREN WITH DUCHENNE MUSCULAR DYSTROPHY

ObjectiveThe goal of our study was to detect the left ventricular functions of duchenne muscular dystrophy (DMD)patients using, pulsed-wave tissue Doppler imaging(PW-TDI, longitudinal strain (LS) and longitudinalstrain rate (LSR) echocardiography who had normalleft ventricular functions in standart echocardiography before, and to match them with the results of thecontrol group.Material and Methodsİn this study compared 32 male patients with DMDwhose mean age was 85.2 ± 38.4 months were matched with 31 healthy males whose mean age was 89.0± 38.9 months. The following demographic featureswere evaluated in both DMD patients and controls:gender, age, body mass index, standard echocardiography parameters, pulsed-wave tissue Doppler imaging (PW-TDI) findings, and two-dimensional (2D) LS/LSR echocardiography measurements.ResultsAsymptomatic boys with DMD were established tohave high heart rate (p

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