Serdal BAŞTUĞ, Hüseyin BAYRAM, Ahmet Göktuğ ERTEM, Abdullah Nabi ASLAN, Zeynep Şeyma TURİNAY, Murat Can GÜNEY, Engin BOZKURT

Tekrarlayan Akut Akciğer Ödemi ile Prezente Olan Dev Bir Papiller Fibroelastom Vakası

Primer intrakardiyak tümörler klinik pratikte nadir görülür ve otopsi serilerinde sıklığının %0.3'ten daha az olduğu bildirilmiştir. Bunların yaklaşık %50'si kardiyak miksomalardır. Papiller fibroelastomlar, kardiyak miksomalardan sonra ikinci en sık görülen primer kardiyak tümörlerdir ve genellikle kalp kapaklarını tutar ve onlara zarar verir. Bu tümörler asemptomatik seyredebileceği gibi ani kardiyak ölüm gibi ciddi sonuçlarla da ilişkili olabilirler. Biz bu vakada, tekrarlayan akut pulmoner ödem ile prezente olan ve mitral arka kapakta papiller fibroelastom tanısı alan 77 yaşında bir erkek hastayı sunduk. ( Sakarya Tıp Dergisi 2016, 6(2):110-114 )

A Huge Papillary Fibroelastoma Case Presenting with Recurrent Acute Pulmonary Edema

Primary intra-cardiac tumors are rare and reported to be less than 0.3% in autopsy series. Approximately 50% of them are cardiac myxomas. Papillary fibroelastomas are the second most common primary cardiac tumors following myxomas and they generally involve and damage the cardiac valves. The clinical presentation of these tumors vary from asymptomatic cases to cases with severe clinical presentation like sudden cardiac death. In this case, we described a 77 years old male patient presenting with recurrent acute pulmonary edema and diagnosed as mitral posterior valve papillary fibroelastoma. ( Sakarya Med J 2016, 6(2):110-114 )

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1. Reynen K. Frequency of primary tumors of the heart. Am J References Cardiol 1996; 77: 107.
2. Gopaldas RR, Atluri PV, Blaustein AS, Bakaeen FG, Huh J, Chu D. Papillary fibroelastoma of the aortic valve: operative approaches upon incidental discovery. Tex Heart Inst J 2009;36:160-63.
3. Ngaage DL, Mullany CJ, Daly RC, Dearani JA, Edwards WD, Tazelaar HD, et al. Surgical treatment of cardiac papillary fibroelastoma: a single center experience with eighty-eight patients. Annals of Thoracic Surgery, 2005;80(5):1712–18.
4. Boodhwani M, Veinot JP, Hendry PJ. Surgical approach to cardiac papillary fibroelastomas. Can J Cardiol 2007; 23(4): 301î2.
5. Sun JP, Asher CR, Yang XS, Cheng GG, Scalia GM, Massed AG, et al. Clinical and echocardiographic characteristics of papillary fibroelastomas: a retrospective and prospective study in 162 patients. Circulation 2001, 103:2687–93.
6. Bruno VD, Mariscalco G, De Vita S, Piffaretti G, Nassiacos D, Sala A. Aortic Valve Papillary Fibroelastoma: a Rare Cause of Angina. Tex Heart Inst J 2011; 38: 456-57.
7. Goda M, Yamazaki I, Suzuki S, Masuda M. Mitral valve papillary fibroelastoma; report of a case. Kyobu Geka 2009;62: 916-19. [In Japanese]
8. Mezilis NE, Dardas PS, Tsikaderis DD. Fibroelastoma of the cardiac valves: a rare cause of embolic stroke. Hellenic J Cardiol 2005; 46: 310-13.
9. Edwards FH, Hale D, Cohen A, Thompson L, Pezzella AT, Virmani R. Primary cardiac valve tumors. Ann Thorac Surg. 1991;52(5):1127-31.
10. Parthenakis F, Nyktari E, Patrianakos A. Asymptomatic papillary fibroelastoma of the Aortic valve in a young woman - a case report. Cardiovasc Ultrasound 2009;7:43.
11. Di Bella G, Masci PG, Ganame J, Dymarkowski S, Bogaert J. Images in cardiovascular medicine. Liquefaction necrosis of mitral annulus calcification: detection and characterization with cardiac magnetic resonance imaging. Circulation. 2008 Mar 25;117(12):e292-94.