Yener AYDIN, Niyazi DİRİ, Aysel KURT, Atila TÜRKYILMAZ, Atilla EROĞLU

İki kardeşte gözlenen konjenital lober amfizem

Konjenital lober amfizem (KLA) genellikle bir lobda hiperinflasyonla karakterizedir. Sol üst lob (%50) ve sağ orta lob (%30) en sık etkilenmekte olup bunu sağ üst lob izlemektedir. Literatürde aile öyküsü ile KLA arasında bir ilişkiden bahsedilmemektedir. Bu makalede sağ üst lobu tutan 3 yaşında bir erkek olgu ile sağ orta lobu tutan 40 günlük kız çocuğu, iki kardeşteki KLA olgusu sunuldu.

Anahtar Kelimeler:

Konjenital lober amfizem, kardeş

Congenital lobar emphysema that seen in two siblings

Congenital lobar emphysema (CLE) is usually characterized by hyper-inflammation in one lobe. The left upper lobe (50%) and the right middle lobe (30%) are most often involved, followed by the right upper lobe. Family history and CLE relation did not mentioned in literature. In this article we present two siblings with CLE; one of them was 3 years old boy with right upper lobe CLE patient and the other one is, his 40 day old sister with right middle lobe CLE.

Keywords:

Congenital lobar emphysema, sibling,

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