Ahmet SERT, Nezire YILMAZ, Murat KONAK, Mehmet OC

Korumasız Triküspid Kapak Orifisinin İki Yeni Olgusu

Korumasız triküspid kapak nadir görülen bir malformasyondur. Triküspid kapak ve subvalvüler aparatın tam veya kısmi agenezisi ile karakterizedir. Triküspid kapak yapılarının tamamen yokluğu genellikle pulmoner atrezi ve sağlam ventriküler septum ile ilişkilidir. Korumasız triküspid kapak orifis tanısı konulan iki vaka bildiriyoruz. Korumasız triküspid kapak orifisi literatürde nadir bildirildiği için bu olgular sunuldu.

Anahtar Kelimeler:

Triküspid kapak, korumasız triküspid orifis, korumasız triküspid orifis

A New Two Cases of Unguarded Tricuspid Valve Orifice

Unguarded tricuspid valve orifice is a rare malformation. It is characterized by complete or partial agenesis of the tricuspid valvular and subvalvular apparatus. The complete absence of tricuspid valve structures is often associated with pulmonary atresia and intact ventricular septum. We report on two cases diagnosed as unguarded tricuspid valve orifice. These cases were presented because of unguarded tricuspid valve orifice is reported rare in the literature

Keywords:

pulmonary atresia, Tricuspid valve, unguarded tricuspid oriﬁce,

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DERGİ MAKALESİ Kanjuh VI, Stevenson JE, Amplatz K, et al. Congenitally unguarded tricuspid orifice with coexistent pulmonary atresia. Circulation. 1964;30:911–917
DERGİ MAKALESİ Anderson RH, Silverman NH, Zuberbuhler JR. Congenitally unguarded tricuspid orifice: its differentiation from Ebstein malformation in association with pulmonary atresia and intact ventricular septum. Pediatr Cardiol. 1990;11(2):86–90
DERGİ MAKALESİ Mohan JC, Shukla M, Mohan V, et al. Congenitally unguarded tricuspid valve orifice with right ventricular apical isolation in an adult. Indian Heart J. 2016;68(2):S121–S125.
İNTERNET DERGİ MAKALESİ Wong KK, Farquharson DI, Duncan WJ. Unguarded tricuspid valvar orifice in the fetus. Cardiol Young. 2004;14(5):557–559.
DERGİ MAKALESİ Shah PM, Raney AA. Tricuspid valve disease. Curr Probl Cardiol 2008; 33: 4
DERGİ MAKALESİ Lamers WH, Viragh S, Wessels A, et al. Formation of the tricuspid valve in the human heart. Circulation 1995; 91: 111– 121.
DERGİ MAKALESİ Attenhofer Jost CH, Connolly HM, Dearani JA, et al. Ebstein's anomaly. Circulation. 2007 Jan 16;115(2):277–85
DERGİ MAKALESİ Celermajer DS, Dodd SM, Greenwald SE, et al. Morbid anatomy in neonates with Ebstein's anomaly of the tricuspid valve: pathophysiologic and clinical implications. J Am Coll Cardiol 1992; 19: 1049– 1053.
DERGİ MAKALESİ Marcus FI, McKenna WJ, Sherrill D, et al. Diagnosis of arrhythmogenic right ventricular cardiomyopathy/dysplasia: proposed modification of the task force criteria. Circulation. (2010) 121:1533–41. 1161/CIRCULATIONAHA.108.840827
American Society of Echocardiography DERNEĞİ KLAVUZU Zoghbi WA, Enriquez-Sarano M, Foster E, et al. American Society of Echocardiography. Recommendations for evaluation of the severity of native valvular regurgitation with two-dimensional and Doppler echocardiography. J Am Soc Echocardiogr 2003; 16: 777-802.
DERGİ MAKALESİ Mohan J.C., Passey R., Arora R. Echocardiographic spectrum of congenitally unguarded tricuspid valve orifice and patent right ventricular outflow tract. Int J Cardiol. 2000;74:153–157.
DERGİ MAKALESİ Mohan J.C., Passey R., Arora R. Congenitally unguarded tricuspid valve orifice with patent right ventricular outflow tract presenting with severe right heart failure of long standing in an adult. Int J Cardiol. 1998;66:85–87.
DERGİ MAKALESİ Mohan J.C., Sengupta P.P., Arora R. Congenitally unguarded tricuspid valve orifice with a giant right atrium and a massive clot in an asymptomatic adult. Indian Heart J. 2001;53:503–504.
DERGİ MAKALESİ Jason L Williams , John L Lockhart , Stephen G Miller ,et al. Left-sided congenitally unguarded tricuspid valve with congenitally corrected transposition of the great arteries: A rare diagnosis confirmed by three-dimensional echocardiography. Echocardiography 2020;37(7):1101-1104
DERGİ MAKALESİ Seneesh Kumar Vikraman , Vipin Chandra, Bijoy Balakrishnan, et al. Unguarded tricuspid orifice: A rare cause of fetal right atrial dilatation with characteristic color doppler sign: Case report with review of literatüre. J Clin Ultrasound 2017;45(6):370-374