Emre EMEKLİ, Mustafa Fuat AÇIKALIN, Melek Kezban GÜRBÜZ, Uğur TOPRAK

Boyunda görülen sinoviyal sarkom olgusu

Sinoviyal sarkomlar artiküler tendonlardan ve eklem kapsüllerinden köken alan nadir malign tümörlerdir. Histolojik olarak sinoviyuma benzerlikleri nedeniyle sinoviyal sarkom olarak isimlendirilmelerine rağmen, nadiren sinoviyal yapı içerirler. Genellikler alt ekstremitede görülmekle birlikte nadir olarak toraks, abdomen, baş-boyun bölgesinde sinoviyal sarkom tespit edilen olgular bildirilmiştir. 60 yaşında erkek hasta boyun sol yarısında şişlik şikayeti ile hastanemize başvurdu. Çekilen bilgisayarlı tomografide sol parafaringeal boşluğu ve sol submandibular fossayı doldurup, farenk lümenine protrude yaklaşık 6,5x5 cm boyutunda kitle tespit edildi. Kitle düzgün sınırlı, ovoid şekilli ve çevre dokulara infiltrasyon göstermemekteydi. Cerrahi olarak total çıkarılan kitlenin histopatolojik tanısı sinovyal sarkom olarak belirlendi. Nadir görülmelerine rağmen sinoviyal sarkomlar Ewing sarkomu, rabdomiyosarkom ve diğer sarkomlarla birlikte kalsifikasyon içeren jukstaartiküler kitlelerin ayırıcı tanısında düşünülmelidir.

Anahtar Kelimeler:

sinoviyal sarkom, bilgisayarlı tomografi, jugulodigastric boşluk, boyun

Synovial sarcoma of the neck

Synovial sarcomas are rare malignant neoplasms commonly arising from articular tendons and joint capsules. Despite being termed synovial sarcomas due to their histologic similarity to the synovium, they rarely involve a synovial structure. Although they mostly occur in lower extremities, rare cases originating from the thorax, abdomen, head, and neck have also been reported. A 60-year-old male patient was admitted to the hospital with a complaint of swelling in left side of the neck. CT revealed a mass of approximately 6.5x5 cm, occupying the left parapharyngeal space and left submandibular fossa and protruding into the pharynx lumen. The lesion was non-infiltrative, well circumscribed, and uniformly ovoid. The patient underwent surgery, and subsequent pathological examination confirmed the diagnosis of synovial sarcoma. Despite their rarity, synovial sarcomas should be considered, along with Ewing’s sarcoma, rhabdomyosarcoma, and other sarcomas, in the differential diagnosis of a large juxtaarticular mass containing calcifications.

Keywords:

synovial sarcoma, computed tomography, jugulodigastric space, neck,

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