SEDAT AKBAŞ, Erol TOY, AHMET SELİM ÖZKAN

Anesthetic management in a patient with Friedreich’s Ataxia: A different approach

ISSN: 2147-0634
Yayın Aralığı: Yılda 4 Sayı
Başlangıç: 2012
Yayıncı: Effect Publishing Agency ( EPA )

Friedreich's Ataxia (FA) is a rare autosomal recessive disease. FA is clinically characterized by progressive ataxia, especially loss of reflex and power in the lower extremities, spasticity and loss of proprioceptive sensory. There is an increased sensitivity to non-depolarizing muscle relaxants in neurodegenerative diseases. Care must be taken of anesthesia management for the use of volatile anesthetics and muscle relaxants, and precautions should be taken for difficult airway management which is due to secondary to kyphoscoliosis and comorbidities. In this case, anesthesia management of emergency operation for septal hematoma by TIVA without using of muscle relaxants and minimalized hemodynamic response depending on the intubation by videolaryngoscope were presented

PDF

___

1. Kurul SH, Yiş U, Güzel Aİ, Kasap H, Başak N, Dirik E. Evaluation Of The Cases With Friedreich Ataxia. Gulhane Med J. 2013;55(2):123-7

2. Elincx-Benizri S, Glik A, Merkel D. et al. Clinical Experience With Deferiprone Treatment for Friedreich Ataxia. J Child Neurol. 2016;31(8):1036-40.

3. Akçaboy ZN, Akçaboy EY, Özek ÖC, Yılmaz AN, Göğüş N. Friedreich ataksisi olan bir hastada anestezik yaklaşim. Türk Anest Rean Der Dergisi. 2011;39(1):50-3.

4. Schmitt HJ, Wick S, Münster T. Rocuronium for muscle relaxation in two children with Friedreich's ataxia. Br J Anaesth. 2004;92(4):592-6.

5. Doğu T, Şahin H, Şimşek T, Altınışık U, Toman H, Altınışık H.B, Erbaş, M. Friedreich ataksili hastada anestezi yönetimi. Abant Med J. 2015;4(3):266-8.

6. Levent K, Yavuz G, Kamil T. Anaesthesia for Friedreich's ataxia. Case report. Minerva Anestesiol. 2000;66(9):657-60