S. Ayvaz AYDOĞDU, Tolga ÜNÜVAR, Ertürk LEVENT, Gülten İNAN

KAWASAKİ HASTALIĞI : İKİ OLGU SUNUMU

Kawasaki hastalığı sistemik bir vaskülittir. En çok orta boy arterleri tutar. Gelişmiş ülkelerde çocuklarda edinselkalp hastalıklarının en sık nedenidir. Halen etiolojisi ve patogenezi tam aydınlatılmamıştır. Koroner arteretkilenmesine bağlı ani ölüm ve kronik hastalık riski intravenöz immünglobulin tedavisi sonrası belirginazalmaktadır. Bu nedenle erken ve doğru tanı prognoz açısından çok önemlidir.Kawasaki hastalığı tanısı konan iki olgumuzun birinde ekokardiyogramda sol ana koroner arterde dilatasyonsaptandı. Diğer olguda kardiyak lezyon yoktu. Koroner arter ektazisi izlemde geriledi. Bu makalede, iki olgunedeniyle Kawasaki hastalığı'nın tanısı, tedavi ve izlem ilkeleri tartışılmıştır

Anahtar Kelimeler:

Kawasaki hastalığı, IVIG, koroner anevrizma

Kawasaki Disease: Report of Two Cases

Kawasaki disease is a systemic vasculitis. It affects medium-sized arteries most commonly. In developed countries, it is the most common reason for acquired cardiac diseases in children. Etiology and pathogenesis of the disease have not yet been completely clarified. Risk of sudden death or chronic cardiac disease due to coronary artery lesions are highly decreased after intravenous immunoglobulin therapy. Thus, early and correct diagnosis is of utmost importance for favorable outcome. In one of the two cases with Kawasaki disease, left main coronary artery was dilated on the echocardiogram. The other patient had no cardiac lesion. Coronary artery ectasia was observed to be regressed. In this paper, due to the two cases, diagnosis, treatment and follow-up principles of Kawasaki disease were discussed.

Keywords:

Kawasaki disease, IVIG, coronary aneurysm,

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