Nilüfer Ekşi DURAN, Yetkin KORKMAZ, Feyza Ballı KURT, Serdar Mustafa YILMAZER, Bekir Yılmaz CİNGÖZBAY

Aort koarktasyonu

Aort koarktasyonu kongenital bir kalp hastalığıdır. Çoğunlukla duktus arteryozusun geriledikten sonra ligamentum arteryosus adını alır aortaya tutunduğu bölgede gelişen segmental bir daralmayı tanımlamaktadır. Duktus arteryosus fetal yaşamda fonksiyone olmayan akciğer fizyolojisi nedeniyle sağ ventriküle gelen kanı pulmoner arterden inen aortaya ileterek normal dolaşımı sağlama görevini yürütmektedir. Aort koarktasyonunda uygun tedavi yaklaşımı tartışmalı olmakla birlikte; cerrahi ve endovasküler girişimler başarıyla uygulanmaktadır. Tedavi edilmemiş vakalarda komplikasyon oranları yüksektir. Bu komplikasyonlar stroke, premature koroner arter hastalığı, serebrovaskuler anevrizma ve aort rüptürüdür. Uzun dönem takipli çalışmalarda; hipertansiyon ve kardiyovaskuler komplikasyonlar nedeni ile başarılı tedaviye rağmen yaşamın beklenildiği gibi uzamadığı saptanmıştır. Bu yazı ağırlıklı olarak erişkin aort koarktasyonu ile ilişkin bir derleme olarak hazırlanmıştır.

Anahtar Kelimeler:

aort koarktasyonu, endovasküler tedavi

Aort coarctation

Coarctation of the aorta is a type of congenital heart disease. Aortic coarctation is a narrowing of the aorta most commonly found in the area where the ductus arteriosus its called ligamentum arteriosum after regression inserts 1 . The ductus arteriosus that is a blood vessel connecting between the pulmonary artery and the proximal descending aorta allows most of the blood from the right ventricle to dessending aorto due to non-functioning lungs in fetal life. Although the appropriate type of treatment for coarctation of the aorta remains somewhat controversial, surgical and endovasculer approach is performed successfully. Complication rate is very high untreated patients. These complications include stroke, early-onset coronary artery disease, and brain aneurysm and aortic rupture. However, several long-term follow-up studies have suggested that despite successful treatment , survival is shorter than expected due to postoperative hypertension and cardiovascular complications.This paper is mainly prepared as a review releated with adult aort coarctation.

Keywords:

aort coarctation, endovascular treatment,

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