Erdem ÖZYURT, Uygar UTKU, Deniz TUNCEL, MUSTAFA GÖKÇE

Travma Sonrası Hirayama Hastalığı: Olgu Sunumu

Hirayama hastalığı karakteristik klinik özellikleri arasında; genç başlangıç, sporadik oluşum, erkeklerde sık görülmesi, kraniyal sinirleri, piramidal yolları, duyusal, serebellar veya ekstra piramidal sistem tutulumu olmadan tek veya iki taraflı üst ekstremite sınırlı kaslarda erime ve güçsüzlük vardır. 22 yaşındaki bayan, alt motor nöron sendromu benzeri sağ tarafta belirgin üst ekstremitelerde yavaş ilerleyen güçsüzlük ile başvurdu. Bir yıl once trafik kazası geçirmişti. Son altı aydır güçsüzlük şikayeti artmıştı. İntervertebral disk hernisi yoktu, ancak; eski travmaya ait bulgular vardı. Burada, biz bir travma sonrası geliştiğini düşündüğümüz nadir bir Hirayama hastalığı olgusu sunduk

Post-traumatic Hirayama Disease: Case Report

The characteristic clinical features of Hirayama disease are young age at onset, sporadic occurrence, male preponderance, wasting and weakness confined to a single or bilaterally upper limb without involvement of cranial nerves, pyramidal tracts, sensory, cerebellar or extrapyramidal systems. A 22-year-old girl was presented with slowly progressive weakness of her upper limbs especially on her right side like a lower motor neuron syndrome. She had a car accident one year ago. She had a complaint of weakness on her left side for last six months. No intervertebral disc herniation was present, but there was an evidence of old traumatic injury. Here, we presented a rare case of Hirayama disease after a trauma

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