Periyodik Ateş Sendromları

ÖzPeriyodik ateş sendromları tanı ve tedavi açısından hekimleri zorlayan heterojen bir grup hastalıkları tanımlamak için kullanılan bir deyimdir. Bu yazıda hiperimmünglobülin D sendromu, tümör nekroz faktör reseptör-1 periyodik sendromu, periyodik ateş, aftöz stomatit, farenjit ve adenit sendromu ve Kriyoprin-ilişkili periyodik sendromları ve diğerleri, klinik, tanı, patogenez ve tedavi yaklaşımları açısından kısaca gözden geçirilmektedir.

Anahtar Kelimeler:

Periyodik ateş, hiperimmünglobülin D, PFAPA sendromu

Periodic Fever Syndromes

AbstractThe periodic syndromes represent a heterogeneous group of disorders that can be very difficult for practicing physicians to diagnosis and treat. This article presents an orderly approach to hyperimmunoglobulin D syndrome; tumor necrosis factor receptor-1 periodic syndrome; periodic fever with aphthous stomatitis, pharyngitis, and adenitis syndrome; and cryopyrin-associated periodic syndromes and others by highlighting the disease presentation, diagnosis, pathogenesis, and treatment.

Keywords:

Pediodic fever, hyperimmunoglobulin D, PFAPAsyndrome,

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