Yesim SENAYLI, Atilla SENAYLI

Xeroderma Pigmentosum Olan Bir Hastada Özofagus Dilatasyonu Yönetimi

Anahtar Kelimeler:

Xeroderma Pigmentosum, yönetim, özofagus dilatasyonu

MANAGEMENT OF A PATIENT WITH XERODERMA PIGMENTOSUM FOR ESOPHAGEAL DILATATION

be a choice for swallowing difficulties of these patients, we could not find a report giving the criterion of the problem. Besides, up to now, xseroderma pigmentosum and esophageal dystonia has not been reported yet. We experienced that patients in this situation could benefit from esophageal dilatation. Also, there has not been much reports giving information in detail for anesthesia management but we suggest that management of these patients within standard anesthetic procedures are not seemed to be harmful in early periods

Keywords:

Xeroderma Pigmentosum, management, esophageal dilatation,

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1- Luron L, Avril MF, Sarasin A, DayaGrosjean L: Prevalence of human papillomavirus in skin tumors from repair deficient xeroderma pigmentosum patients. Cancer Letters 2007; 250: 213–219.
2- Kraemer KH Patronas NJ, Schıffmann R, Brooks BP, Tamura D, Dıgıovanna JJ: Xeroderma Pıgmentosum, Trıchothıodystrophy And Cockayne Syndrome: A Complex Genotype– Phenotype Relatıonship. Neuroscience 2007; 145: 1388–1396.
3- Brooks PJ: The Case For 8,5’- Cyclopurıne-2’-Deoxynucleosıdes As Endogenous DNA Lesions That Cause Neurodegeneration In Xeroderma Pigmentosum. Neuroscience 2007; 145: 1407–1417.
4- Muto A, Matsui A, Saito Y, Iwamoto H, Kaneko K, Masuko K, Chikumaru Y, Saito K, Kimura S: Laryngeal dystonia in xeroderma pigmentosum. Brain & Development 2005; 27: 598– 601.
5- Masuda Y, Imaizumi H, Okanuma M, Narimatsu E, Asai Y, Namiki A: Anesthesia for a patient with xeroderma pigmentosum. Masui 2002; 51:169-71.
6- Miyazaki R, Nagata T, Kai T, Takahashi S: Anesthesia for a patient with xeroderma pigmentosum. Masui 2007; 56: 439-41.
7- Brunner T, Jöhr M: Anesthetic management of a child with xeroderma pigmentosum. Pediatric Anesthesia 2004; 14: 697–698.